MedPath

Clinical Study Assessing the Efficacy and Safety of Macitentan in Fontan-palliated Subjects

Phase 3
Completed
Conditions
Congenital Heart Disease
Interventions
Registration Number
NCT03153137
Lead Sponsor
Actelion
Brief Summary

The primary objective is to assess the effect of macitentan 10 mg as compared to placebo on exercise capacity through cardiopulmonary exercise testing.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
142
Inclusion Criteria
  • Written informed consent/assent from the subject and/or a legal representative prior to initiation of any study-mandated procedures
  • Fontan-palliated subjects with either intra-atrial lateral tunnel total cavopulmonary connection (LT-TCPC), or extra cardiac tunnel TCPC (EC-TCPC) surgery > 1 year before Screening. Either LT- or EC-TCPC can be primary or secondary to atrio-pulmonary connection
  • New York Heart Association (NYHA) functional class (FC) II or III (assessed by the investigator using the Specific Activity Scale
  • Women of childbearing potential must have a negative serum pregnancy test use reliable contraception
Exclusion Criteria
  • Pattern of Fontan circulation severity
  • Deterioration of the Fontan-palliated condition.
  • Limitations to Cardiopulmonary exercise testing (CPET)
  • Peak VO2 < 15 mL/kg/min.
  • Any known factor or disease that may interfere with treatment compliance or full participation in the study

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
MacitentanMacitentan 10 mgMacitentan 10 mg per day; film-coated tablet; oral use
PlaceboPlacebofilm-coated tablet; oral use
Primary Outcome Measures
NameTimeMethod
Change From Baseline in Peak Oxygen Uptake/Consumption (VO2) Up to Week 16Baseline up to Week 16

Change from baseline in peak VO2 up to Week 16 was reported.

Secondary Outcome Measures
NameTimeMethod
Change From Baseline in Glucose, Cholesterol, Triglycerides, Sodium, Potassium, Chloride and CalciumBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in glucose, cholesterol, triglycerides, sodium, potassium, chloride and calcium was reported.

Change From Baseline in Alpha FetoproteinBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in alpha fetoprotein was reported.

Change From Baseline in Mean Count Per Minute of Daily Physical Activity Measured by Accelerometer (PA-Ac) Up to Week 16Baseline up to Week 16

Change from baseline in mean count per minute of daily PA-Ac up to Week 16 was reported. The daily physical activity (counts per min) of the participant was assessed via accelerometer during daytime. The accelerometer was given to the participant at Visit 1, and data was collected for 9 consecutive daily daytime periods after Visit 1 (baseline) to Visit 4 (Week 16).

Number of Participants With AEs Leading to Premature Discontinuation of Study TreatmentUp to 56 weeks

Number of participants with AEs leading to premature discontinuation of study treatment was reported. AEs leading to premature discontinuation of study treatment were those with action taken with study drug reported as 'permanently discontinued' by the investigator.

Change From Baseline in Erythrocytes and ReticulocytesBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in erythrocytes and reticulocytes at Week 8, Week 16, Week 32 and Week 52 was reported.

Change From Baseline in Gamma Glutamyl TransferaseBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in gamma glutamyl transferase was reported.

Change From Baseline in Albumin and ProteinBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in albumin and protein was reported.

Change From Baseline in Peak VO2 Up to Week 52Baseline up to Week 52

Change from baseline in peak VO2 up to Week 52 was reported.

Change From Baseline in HemoglobinBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in hemoglobin was reported.

Change From Baseline in HematocritBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in hematocrit was reported.

Change From Baseline in Bilirubin and Direct BilirubinBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in bilirubin and direct bilirubin was reported.

Change From Baseline in CreatinineBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in creatinine was reported.

Change From Baseline in UrateBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in urate was reported.

Change From Baseline in Cystatin CBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in cystatin C was reported.

Number of Participants With Treatment-emergent Serious Adverse Events (SAEs)Up to 56 weeks

SAE is any AE that results in: death, persistent or significant disability/incapacity, requires inpatient hospitalization or prolongation of existing hospitalization, is life-threatening experience, is a congenital anomaly/birth defect and may jeopardize participant and/or may require medical or surgical intervention to prevent one of the outcomes listed above.

Change From Baseline in Pulse RateBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in pulse rate at Week 8, Week 16, Week 32 and Week 52 was reported.

Change From Baseline in Leucocytes, Neutrophils, Lymphocytes, Monocytes, Eosinophils, Basophils and PlateletsBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in leucocytes, neutrophils, lymphocytes, monocytes, eosinophils, basophils and platelets at Week 8, Week 16, Week 32 and Week 52 was reported.

Change From Baseline in Alanine Aminotransferase (ALT), Aspartate Aminotransferase (AST) and Alkaline Phosphatase (AP)Baseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in ALT, AST and AP were reported.

Change From Baseline in Prothrombin TimeBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in prothrombin time was reported.

Number of Participants With Treatment-emergent Adverse Events (AEs)Up to 56 weeks

An adverse event is any untoward medical event that occurs in a participant administered an investigational product, and it does not necessarily indicate only events with clear causal relationship with the relevant investigational product.

Change From Baseline in Systolic and Diastolic Arterial Blood Pressure (BP)Baseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in systolic and diastolic arterial BP at Week 8, Week 16, Week 32 and Week 52 was reported.

Change From Baseline in Oxygen Saturation (SpO2)Baseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in SpO2 was reported.

Change From Baseline in Body WeightBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in body weight was reported.

Number of Participants With Treatment-emergent Markedly Abnormal Laboratory ValuesUp to 56 weeks

Number of participants with treatment-emergent markedly laboratory abnormal laboratory values were reported. Abnormal values for platelets (LL \< 75); Lymphocytes (HH \> 4.0); Neutrophils (LL \< 1.5); Prothrombin International Normalized Ratio: HH (greater than and equal to \[\>=\] 1.5 upper limit of normal \[ULN\]), Ratio: HH \>= 2.5 ULN); Bilirubin (HH \>= 2 ULN); Alkaline Phosphatase (HH \> 2.5 ULN); Glomerular Filtration Rate (LL \< 60); Glucose (HH \> 8.9); Triglycerides (HH \> 3.42). Here "HH" refers to values above the normal range, where H stands for "high" and "LL" refers to values below the normal range where L stands for "low".

Change From Baseline in Prothrombin International Normalized RatioBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in prothrombin international normalized ratio was reported.

Change From Baseline in Urea NitrogenBaseline, Week 8, Week 16, Week 32 and Week 52

Change from baseline in urea nitrogen was reported.

Trial Locations

Locations (32)

University of Alabama at Birmingham

🇺🇸

Birmingham, Alabama, United States

UCLA

🇺🇸

Los Angeles, California, United States

Massachusetts General Hospital Heart Center

🇺🇸

Boston, Massachusetts, United States

Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Texas Children's Hospital

🇺🇸

Houston, Texas, United States

Providence Medical Research Providence Health Care

🇺🇸

Spokane, Washington, United States

Royal Adelaide Hospital

🇦🇺

Adelaide, Australia

Royal Prince Alfred Hospital

🇦🇺

Camperdown, Australia

The Prince Charles Hospital, Adult Congenital Heart Disease Unit

🇦🇺

Chermside, Australia

Royal Children's Hospital

🇦🇺

Parkville, Australia

Queensland CHILDREN'S HOSPITAL

🇦🇺

South Brisbane, Australia

Westmead Hospital

🇦🇺

Westmead, Australia

CHU de Quebec Universite Laval

🇨🇦

Quebec, Canada

Beijing Anzhen Hospital

🇨🇳

Beijing, China

Beijing Fuwai Hospital

🇨🇳

Beijing, China

Shanghai Childrens Medical Center

🇨🇳

Shanghai, China

Wuhan Asia Heart Hospital

🇨🇳

Wuhan, China

Fakultni nemocnice v Motole

🇨🇿

Praha 5, Czechia

Rigshospitalet Kardiologisk Klinisk

🇩🇰

Copenhagen, Denmark

CHU Arnaud de Villeneuve

🇫🇷

Montpellier Cedex 5, France

Hôpital Necker - Enfants Malades

🇫🇷

Paris, France

Hôpital Cardiologique Du Haut-Lévêque

🇫🇷

Pessac, France

Deutsches Herzzentrum Berlinklinik Für Angeborene Herzfehler

🇩🇪

Berlin, Germany

Deutsches Herzzentrum München

🇩🇪

München, Germany

Auckland City Hospital

🇳🇿

Auckland, New Zealand

Uniwersyteckie Centrum Kliniczne

🇵🇱

Gdansk, Poland

Uniwersytecki Szpital Dzieciecy w Krakowie

🇵🇱

Krakow, Poland

Krakowski Szpital Specjalityczny im Jana Pawla II Oddzial Kliniczny Chorob Serca i Naczyn

🇵🇱

Krakow, Poland

Wojewodzki Szpital Specjalistyczny We Wroclawiu

🇵🇱

Wroclaw, Poland

National Taiwan University Hospital

🇨🇳

Taipei, Taiwan

Queen Elizabeth Hospital

🇬🇧

Birmingham, United Kingdom

Birmingham Children's Hospital

🇬🇧

Birmingham, United Kingdom

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