MedPath

A Phase 2 Study to Evaluate Efficacy and Safety of VX-561 in Subjects Aged 18 Years and Older With Cystic Fibrosis

Phase 2
Completed
Conditions
Cystic Fibrosis
Interventions
Drug: IVA
Drug: Placebo
Registration Number
NCT03911713
Lead Sponsor
Vertex Pharmaceuticals Incorporated
Brief Summary

The purpose of this study is to evaluate the efficacy, safety, pharmacodynamic (PD) and pharmacokinetic (PK) effect of VX-561.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
77
Inclusion Criteria
  • Must have 1 of the following 9 CFTR mutations on at least 1 allele: G551D, G178R, S549N, S549R, G551S, G1244E, S1251N, S1255P, or G1349D
  • On ivacaftor therapy
  • FEV1 value ≥40% and ≤100% of predicted mean for age, sex, and height

Key

Exclusion Criteria
  • History of clinically significant cirrhosis with or without portal hypertension
  • History of solid organ or hematological transplantation
  • Lung infection with organisms associated with a more rapid decline in pulmonary status

Other protocol defined Inclusion/Exclusion criteria may apply

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
VX-561: 250 mgPlaceboParticipants received VX-561 250 mg orally qd in the treatment period for 12 weeks.
VX-561: 150 mgPlaceboParticipants received VX-561 150 mg orally qd in the treatment period for 12 weeks.
VX-561: 25 mgPlaceboParticipants received VX-561 25 mg orally daily (qd) in the treatment period for 12 weeks.
VX-561: 250 mgVX-561Participants received VX-561 250 mg orally qd in the treatment period for 12 weeks.
IvacaftorIVAParticipants received IVA 150 milligrams (mg) orally every 12 hours (q12h) in the treatment period for 12 weeks.
IvacaftorPlaceboParticipants received IVA 150 milligrams (mg) orally every 12 hours (q12h) in the treatment period for 12 weeks.
VX-561: 50 mgVX-561Participants received VX-561 50 mg orally qd in the treatment period for 12 weeks.
VX-561: 50 mgPlaceboParticipants received VX-561 50 mg orally qd in the treatment period for 12 weeks.
VX-561: 25 mgVX-561Participants received VX-561 25 mg orally daily (qd) in the treatment period for 12 weeks.
VX-561: 150 mgVX-561Participants received VX-561 150 mg orally qd in the treatment period for 12 weeks.
Primary Outcome Measures
NameTimeMethod
Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)From Baseline at Week 12

FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration.

Secondary Outcome Measures
NameTimeMethod
Absolute Change in Sweat Chloride (SwCl)From Baseline at Week 12

Sweat samples were collected using an approved collection device.

Observed Pre-Dose Concentration (Ctrough) of VX-561 and Its Metabolites (M1-VX-561 and M6-VX-561) and IVA and Its Metabolites (M1-IVA and M6-IVA)At Week 4
Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (AEs) and Serious Adverse Events (SAEs)Baseline up to Week 16

Trial Locations

Locations (48)

University of Alabama at Birmingham

🇺🇸

Birmingham, Alabama, United States

Banner University of Arizona Medical Center

🇺🇸

Tucson, Arizona, United States

Miller Children's Hospital / Long Beach Memorial

🇺🇸

Long Beach, California, United States

UCSF Gateway Medical Center

🇺🇸

San Francisco, California, United States

National Jewish Health

🇺🇸

Denver, Colorado, United States

University of Miami Miller School of Medicine

🇺🇸

Miami, Florida, United States

Central Florida Pulmonary Group, PA

🇺🇸

Orlando, Florida, United States

Indiana University

🇺🇸

Indianapolis, Indiana, United States

University of Kansas Medical Center

🇺🇸

Kansas City, Kansas, United States

University of Kentucky

🇺🇸

Lexington, Kentucky, United States

Scroll for more (38 remaining)
University of Alabama at Birmingham
🇺🇸Birmingham, Alabama, United States

MedPath

Empowering clinical research with data-driven insights and AI-powered tools.

© 2025 MedPath, Inc. All rights reserved.