MedPath

Efficacy and Safety of AG10 in Subjects With Transthyretin Amyloid Cardiomyopathy

Phase 3
Completed
Conditions
Transthyretin Amyloidosis
Amyloidosis
Amyloid Cardiomyopathy
Cardiomyopathies
Heart Diseases
Interventions
Drug: Placebo Oral Tablet
Registration Number
NCT03860935
Lead Sponsor
Eidos Therapeutics, a BridgeBio company
Brief Summary

Phase 3 efficacy and safety study to evaluate acoramidis (AG10) HCl 800 mg administered orally twice a day compared to placebo in subjects with symptomatic Transthyretin Amyloid Cardiomyopathy (ATTR-CM).

Detailed Description

Transthyretin amyloid cardiomyopathy (ATTR-CM) is an underdiagnosed condition believed to affect more than 400,000 people worldwide. In ATTR-CM, the accumulation of transthyretin (TTR) amyloid results in thickening and stiffening of the heart, which often leads to heart failure or even death.

There are two forms of ATTR-CM:

* Wild Type\* This form of the condition primarily develops in older individuals who do not carry gene mutations.

* Hereditary\* This form of the condition comes from gene mutations passed down in families.

In this study we are researching the investigational drug acoramidis HCl 800 mg administered orally twice a day. Through the study, we want to evaluate the efficacy and safety of acoramidis in patients with ATTR-CM versus placebo.

This is a 30 month, randomized, double-blind, placebo-controlled study. This means that, during the 30 month study, investigators conducting the research and study participants will not know whether the study participant is receiving acoramidis or placebo.

The primary outcomes of the study are:

1. The impact of acoramidis versus placebo on the change in distance walked on the 6 minute walk test (6MWT) after 12 months of treatment compared to baseline.

2. The impact of acoramidis versus placebo on the hierarchical combination of All-Cause mortality, cumulative frequency of cardiovascular-related hospitalizations, change from baseline in NT-proBNP, and change in from baseline in 6MWT over a 30-month fixed treatment duration.

At the end of 30 months, participants may be eligible to receive investigational acoramidis, and there is no placebo. This is called an "open label extension." This separate study may help us better understand the safety related to taking acoramidis over a longer period of time.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
632
Inclusion Criteria
  • Have an established diagnosis of ATTR-CM with either wild-type TTR or variant TTR genotype
  • Have a history of heart failure evidenced by at least one prior hospitalization for heart failure or clinical evidence of heart failure without prior heart failure hospitalization manifested by signs or symptoms of volume overload or elevated intracardiac pressures or heart failure symptoms that required or require ongoing treatment with a diuretic.
  • New York Heart Association (NYHA) Class I-III symptoms due to ATTR cardiomyopathy.
  • On stable doses of cardiovascular medical therapy
  • Completed ≥150 m on the 6MWT on 2 tests that are within 15% of total distance walked prior to randomization
  • Biomarkers of myocardial wall stress, NT-proBNP level ≥300 pg/mL at screening
  • Have left ventricular wall (interventricular septum or left ventricular posterior wall) thickness ≥12 mm
Exclusion Criteria
  • Had acute myocardial infarction, acute coronary syndrome or coronary revascularization, or experienced stroke or transient ischemic attack within 90 days prior to screening
  • Has hemodynamic instability
  • Likely to undergo heart transplantation within a year of screening
  • Confirmed diagnosis of primary (light chain) amyloidosis
  • Biomarkers of myocardial wall stress, NT-proBNP level ≥8500 pg/mL at screening
  • Measure of kidney function, eGFR by MDRD formula <15 mL/min/1.73 m2
  • Current treatment with marketed drug products and other investigational agents for the treatment of ATTR-CM
  • Current treatment with calcium channel blockers with conduction system effects (e.g. verapamil, diltiazem). The use of dihydropyridine calcium channel blockers is allowed. The use of digitalis will only be allowed if required for management of atrial fibrillation with rapid ventricular response

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
PlaceboPlacebo Oral TabletSubjects will receive placebo to match twice daily. 6MWT primary outcome will be assessed at the end of 12 months. The hierarchical combination of All-Cause mortality, cumulative frequency of cardiovascular-related hospitalizations, change from baseline in NT-proBNP levels, and change from baseline in distance walked on the 6MWT will be assessed after 30 months of treatment.
acoramidis HCl 800 mgacoramidisSubjects will receive acoramidis HCl 800 mg twice daily. 6MWT primary outcome will be assessed at the end of 12 months. The hierarchical combination of All-Cause mortality, cumulative frequency of cardiovascular-related hospitalizations, change from baseline in NT-proBNP levels, and change from baseline in distance walked on the 6MWT will be assessed after 30 months of treatment.
Primary Outcome Measures
NameTimeMethod
A Hierarchical Combination of All-Cause Mortality, Cumulative Frequency of CV-related Hospitalization, Change From Baseline in NT-proBNP and Change From Baseline in 6MWT at the Last Available Visit Where Both Subjects Had Non-missing Assessments.Baseline up to Month 30

The endpoint was analyzed using Finkelstein-Schoenfeld method. The method combines all-cause mortality, cumulative frequency of CV-related hospitalizations, change from baseline in NT-proBNP and change from baseline in 6MWT in a hierarchical fashion. The method compares every participant with every other participant within strata, assigning a +1 to the "better" participant and a -1 to the "worse" participant and 0 if they are "tied". Participants who had heart transplantation or implantation of a cardiac mechanical assist device were handled in the same manner as death. 'Win' represents a participant doing better based on hierarchical comparison. The reported unit is the total percent of "wins" for each treatment group from performing such a hierarchical comparison across stratification factors in the study.

Secondary Outcome Measures
NameTimeMethod
Change From Baseline to Month 30 in the Distance Walked During the 6 Minute Walk Test (6MWT)Month 30

6MWT measures the total distance that a participant could walk in 6 minutes. Participants were asked to perform the test at a pace that was comfortable to them, with as many breaks as they needed.

Change From Baseline to Month 30 of the Kansas City Cardiomyopathy Questionnaire Overall Score (KCCQ-OS)Month 30

KCCQ is a 23-item participant-completed questionnaire that assesses health status and health-related quality of life in participants with heart failure. Eight domain scores were calculated for the KCCQ: Physical limitation, Social limitation, Quality of life, Self-efficacy, Symptom stability, Symptom frequency, Symptom burden, and Total symptoms (calculated as the mean of Symptom frequency and Symptom burden scores). The summary score of Overall Summary (calculated as mean of Physical limitation, Social limitation, Total symptoms, and Quality of life scores) was calculated. Domain and summary scores were scaled to range from 0 (minimum) to 100 (maximum); higher scores represent better health status.

Change From Baseline to Month 30 in Serum TTR (Prealbumin) LevelMonth 30

Serum TTR (Prealbumin) is an in vivo biomarker of stabilization.

All-cause Mortality by Month 30, Including Death Due to Any Cause, Heart Transplant or Cardiac Mechanical Assist Device (CMAD)Baseline up to Month 30

Number of deaths due to any cause was analyzed. Participants who had heart transplantation or implantation of a CMAD were handled in the same manner as death.

Trial Locations

Locations (103)

Piedmont Heart Institute Athens

🇺🇸

Athens, Georgia, United States

Northwestern University

🇺🇸

Chicago, Illinois, United States

The University of Chicago Medical Center

🇺🇸

Chicago, Illinois, United States

NorthShore University Health System

🇺🇸

Evanston, Illinois, United States

MedStar Medical Group Cardiology at Franklin Square Medical Center

🇺🇸

Baltimore, Maryland, United States

Saint Elizabeth's Medical Center

🇺🇸

Boston, Massachusetts, United States

North Shore University Hospital

🇺🇸

Manhasset, New York, United States

Cleveland Clinic

🇺🇸

Cleveland, Ohio, United States

Hospital Cárdio Pulmonar

🇧🇷

Salvador, Bahia, Brazil

Royal Free Hospital

🇬🇧

London, England, United Kingdom

Box Hill Hospital

🇦🇺

Box Hill, Australia

Royal Adelaide Hospital

🇦🇺

Adelaide, Australia

Royal Hobart Hospital

🇦🇺

Hobart, Australia

Universita degli Studi di Roma La Sapienza - Umberto I Policlinico di Roma

🇮🇹

Roma, Italy

Waikato Hospital

🇳🇿

Hamilton, Waikato, New Zealand

Indiana University

🇺🇸

Indianapolis, Indiana, United States

University of Miami - Sylvester Comprehensive Cancer Center

🇺🇸

Miami, Florida, United States

University of Washington School of Medicine

🇺🇸

Seattle, Washington, United States

Cedars-Sinai Medical Center

🇺🇸

Los Angeles, California, United States

Pacific Heart Institute

🇺🇸

Santa Monica, California, United States

Emory Heart and Vascular Center

🇺🇸

Atlanta, Georgia, United States

Washington University School of Medicine

🇺🇸

Saint Louis, Missouri, United States

New York University Langone Health

🇺🇸

New York, New York, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

Mount Sinai Hospital

🇺🇸

New York, New York, United States

Laurelton Heart Specialist

🇺🇸

Rosedale, New York, United States

Penn Presbyterian Medical Center

🇺🇸

Philadelphia, Pennsylvania, United States

Allegheny General Hospital

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Pittsburgh

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Texas Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

Carilion Clinic Roanoke Heart Institute

🇺🇸

Roanoke, Virginia, United States

Providence Sacred Heart Medical Center

🇺🇸

Spokane, Washington, United States

Duke University Health System

🇺🇸

Durham, North Carolina, United States

University of Utah

🇺🇸

Salt Lake City, Utah, United States

Santa Casa de Misericordia - Porto Alegre

🇧🇷

Porto Alegre, Rio Grande Do Sul, Brazil

MedStar Washington Hospital Center

🇺🇸

Washington, District of Columbia, United States

Toronto Heart Centre

🇨🇦

Toronto, Ontario, Canada

Universitair Ziekenhuis Leuven

🇧🇪

Leuven, Belgium

INCOR

🇧🇷

São Paulo, Sao Paulo, Brazil

Centro Hospitalar de Lisboa Norte EPE- Hospital Santa Maria

🇵🇹

Lisboa, Portugal

Centro Hospitalar do Porto

🇵🇹

Porto, Portugal

Newark Beth Israel Medical Center

🇺🇸

Newark, New Jersey, United States

University of Calgary

🇨🇦

Calgary, Alberta, Canada

CAPED - Centro Avançado de Pesquisa e Estudos para o Diagnóstico

🇧🇷

Ribeirão Preto, Sao Paulo, Brazil

Azienda Ospedaliero Universitaria di Bologna Policlinico Sant'Orsola-Malpighi

🇮🇹

Bologna, Italy

Universitair Medisch Centrum Utrecht

🇳🇱

Utrecht, Netherlands

Montreal Heart Institute

🇨🇦

Montréal, Canada

Ospedale San Donato

🇮🇹

Arezzo, Italy

University of British Columbia

🇨🇦

Vancouver, British Columbia, Canada

Universitair Medisch Centrum Groningen

🇳🇱

Groningen, Netherlands

National Institute of Cardiology

🇵🇱

Warsaw, Poland

Prisma Health - Greenville Memorial Hospital

🇺🇸

Greenville, South Carolina, United States

Boston University School of Medicine

🇺🇸

Boston, Massachusetts, United States

Instituto de Cardiologia do Rio Grande do Sul

🇧🇷

Porto Alegre, Brazil

Centre Hospitalier de L'Universite de Montreal - Hôpital Notre-Dame

🇨🇦

Montréal, Quebec, Canada

Hadassah University Hospital Ein Kerem

🇮🇱

Jerusalem, Israel

Maastricht Universitair Medisch Centrum

🇳🇱

Maastricht, Limburg, Netherlands

Seoul National University Hospital

🇰🇷

Seoul, Gyeonggi-Do, Korea, Republic of

Mayo Clinic

🇺🇸

Rochester, Minnesota, United States

Oregon Health and Science University

🇺🇸

Portland, Oregon, United States

Fiona Stanley Hospital

🇦🇺

Murdoch, Australia

Saint Vincent's Hospital Sydney

🇦🇺

Sydney, Australia

Princess Alexandra Hospital

🇦🇺

Woolloongabba, Australia

Ziekenhuis Oost-Limburg - Campus Sint-Jan

🇧🇪

Genk, Limburg, Belgium

Jessa Ziekenhuis - Campus Virga Jesse

🇧🇪

Hasselt, Limburg, Belgium

Algemeen Ziekenhuis Sint-Jan Brugge-Oostende

🇧🇪

Brugge, West Vlaanderen, Belgium

Onze-Lieve-Vrouw Ziekenhuis Aalst

🇧🇪

Aalst, Belgium

CancerCare Manitoba - St. Boniface

🇨🇦

Winnipeg, Manitoba, Canada

University of Toronto

🇨🇦

Toronto, Ontario, Canada

Halifax Infirmary

🇨🇦

Halifax, Nova Scotia, Canada

Hôpital du Sacré-Coeur de Montréal

🇨🇦

Montréal, Quebec, Canada

General University Hospital in Prague

🇨🇿

Nové Město, Czechia

Institut Universitaire de Cardiologie et de Pneumologie de Québec

🇨🇦

Quebec City, Quebec, Canada

Hôpital régional de Rimouski

🇨🇦

Rimouski, Quebec, Canada

St. Anne´s University Hospital

🇨🇿

Brno Střed, Czechia

Institute for Clinical and Experimental Medicine

🇨🇿

Prague, Czechia

Aarhus Universitetshospital

🇩🇰

Aarhus, Dinamarca, Denmark

Mater Misericordiae University Hospital

🇮🇪

Dublin, Ireland

Alexandra General Hospital of Athens

🇬🇷

Athens, Attica, Greece

Saint Vincents University Hospital

🇮🇪

Dublin, Ireland

The Chaim Sheba Medical Center

🇮🇱

Tel Hashomer, Israel

Fondazione IRCCS Policlinico San Matteo

🇮🇹

Pavia, Italy

Azienda Ospedaliero - Universitaria Careggi

🇮🇹

Firenze, Italy

Seoul National University Bundang Hospital

🇰🇷

Seongnam-si, Gyeonggi-Do, Korea, Republic of

Fondazione Toscana Gabriele Monasterio per la Ricerca Medica e di Sanità Pubblica

🇮🇹

Pisa, Italy

Middlemore Hospital

🇳🇿

Otahuhu, Auckland, New Zealand

Ospedale degli Infermi

🇮🇹

Rimini, Italy

Clínica Universidad de Navarra

🇪🇸

Pamplona, Navarra, Spain

Clinica Universidad de Navarra Madrid

🇪🇸

Madrid, Spain

Hospital Universitari Germans Trias i Pujol

🇪🇸

Barcelona, Spain

Hospital Juan Ramón Jiménez

🇪🇸

Huelva, Spain

Hospital Universitario Puerta de Hierro

🇪🇸

Madrid, Spain

Hospital Son Llàtzer

🇪🇸

Palma De Mallorca, Spain

Hospital Clínico Universitario de Santiago de Compostela

🇪🇸

Santiago De Compostela, Spain

Richmond Pharmacology

🇬🇧

London, United Kingdom

Hospital Clínico Universitario de Valencia

🇪🇸

Valencia, Spain

University of Colorado Hospital - Anschutz Medical Campus

🇺🇸

Aurora, Colorado, United States

University of North Carolina - Chapel Hill

🇺🇸

Chapel Hill, North Carolina, United States

Virginia Commonwealth University Medical Center

🇺🇸

Richmond, Virginia, United States

Yale School of Medicine

🇺🇸

New Haven, Connecticut, United States

The Medical University of South Carolina

🇺🇸

Charleston, South Carolina, United States

Saint Luke's Hospital - Kansas City

🇺🇸

Kansas City, Missouri, United States

Montefiore Medical Center

🇺🇸

Bronx, New York, United States

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