MedPath

Study Comparing Efficacy and Safety of Defibrotide vs Best Supportive Care in the Prevention of Hepatic Veno-Occlusive Disease in Adult and Pediatric Patients

Phase 3
Completed
Conditions
Veno-occlusive Disease
Interventions
Other: Best Supportive Care
Registration Number
NCT02851407
Lead Sponsor
Jazz Pharmaceuticals
Brief Summary

This study is to compare the efficacy and safety of defibrotide prophylaxis in addition to best supportive care versus best supportive care alone in the prevention of hepatic veno- occlusive disease (VOD) in adult and pediatric patients undergoing hematopoietic stem cell transplant who are at high risk or very high risk of developing VOD.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
372
Inclusion Criteria
  1. Patient must be above the age of 1 month as of the start date of study treatment.
  2. Patient must be scheduled to undergo allogeneic hematopoietic stem cell transplant (HSCT) (adults or pediatric patients) or autologous HSCT (pediatric patients only) and be at high risk or very high risk of developing veno-occlusive disease (VOD).
  3. Female patients (and female partners of male patients) of childbearing potential who are sexually active must agree to use a highly effective method of contraception with their partners during exposure to defibrotide and for 1 week after the last dose of defibrotide.
  4. Adult patients must be able to understand and sign a written informed consent. For minor patients, the parent/legal guardian or representative must be able to understand and sign a written informed consent. Assent, when appropriate, will be obtained according to institutional guidelines.
Exclusion Criteria
  1. Patient has hemodynamic instability within 24 hours before the start of study treatment.
  2. Patient has acute bleeding that is clinically significant within 24 hours before the start of study treatment.
  3. Patient used any medication that increases the risk of bleeding within 24 hours before the start of study treatment.
  4. Patient is using or plans to use an investigational agent for the prevention or treatment of VOD.
  5. Patient, in the opinion of the investigator, may not be able to comply with the safety monitoring requirements of the study.
  6. Patient or parent/legal guardian or representative has a psychiatric illness that would prevent the patient or parent/legal guardian or representative from giving informed consent and/or assent.
  7. Patient has a serious active disease or co-morbid medical condition, as judged by the investigator, which would interfere with the conduct of this study.
  8. Patient is pregnant or lactating and does not agree to stop breastfeeding.
  9. Patient has a known history of hypersensitivity to defibrotide or any of the excipients.
  10. Patient or parent/legal guardian or representative lacks the full mental capacity to understand and sign a written informed consent.
  11. Patient is receiving or plans to receive other investigational therapy during study.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Best Supportive CareBest Supportive CareBest supportive care alone (without the addition of defibrotide) according to institutional guidelines and patient need, is administered on the first day of conditioning and will continue until Day +30 post HSCT or hospital discharge, whichever is sooner, or diagnosis of VOD, if applicable
DefibrotideDefibrotideDefibrotide is administered intravenously at a dose of 25 mg/kg/day in addition to best supportive care on the day before the first day of the conditioning regimen and will continue (for those patients without a VOD diagnosis) for a recommended minimum of 21 days and end no later than Day +30 post HSCT
Primary Outcome Measures
NameTimeMethod
Veno-occlusive Disease (VOD)-Free Survival by Day +30 Post-Hematopoietic Stem Cell Transplant (HSCT) Per the Independent Endpoint Adjudication Committee (EPAC)Day +30 Post-HSCT

VOD-free survival is a composite of survival status and VOD occurrence as determined by modified Seattle criteria adjudicated by a blinded independent EPAC. An event is defined as a VOD diagnosis (as assessed by the EPAC) or death, whichever, is earlier, up to and including Day +30 post-HSCT. The values reported below are participants who did not experience VOD or death by Day +30 post-HSCT.

Secondary Outcome Measures
NameTimeMethod
Veno-Occlusive Disease (VOD)-Free Survival by Day +100 Post-Hematopoietic Stem Cell Transplant (HSCT) Per the Independent Endpoint Adjudication Committee (EPAC)Day +100 Post-HSCT

VOD-free survival is a composite of survival status and VOD occurrence as determined by modified Seattle criteria adjudicated by a blinded independent EPAC. An event is defined as a VOD diagnosis (as assessed by the EPAC) or death, whichever, is earlier, up to and including Day +100 post-HSCT. The values reported below are participants who did not experience VOD or death by Day +100 post-HSCT.

Percentage of Participants With Veno-Occlusive Disease (VOD) by Day +30 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +30 Post-HSCT

The number of participants who were diagnosed with VOD based on the Modified Seattle Criteria as per blinded EPAC assessment. The percentage was calculated out of the total number of participants in each arm of the study. The values reported below are the numbers and percentages of participants who experienced VOD by Day +30 post-HSCT.

Veno-Occlusive Disease (VOD)-Free Survival Rate by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

VOD-free survival is a composite of survival status and VOD occurrence as determined by modified Seattle criteria. An event is defined as a VOD diagnosis or death, whichever, is earlier, up to and including Day +180 post-HSCT. The diagnosis of VOD through Day +100 post-HSCT was based on Endpoint Adjudication Committee (EPAC), and the diagnosis of VOD after Day +100 post-HSCT was based on investigator assessments. The values reported below are participants who did not experience VOD or death by Day +180 post-HSCT.

Non-Relapse Mortality (NRM) for Defibrotide (DP) and Best Supportive Care (BSC) by Days +100 and +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Days +100 and +180 Post-HSCT

NRM is defined as death that occurs after HSCT in participants who were noted as having malignant primary disease on the disease history electronic case report form (eCRF) and do not have primary disease relapse post-HSCT.

Percentage of Participants With Veno-Occlusive Disease (VOD)-Associated Multi-Organ Dysfunction (MOD) by Days +30 and Days +100 Post-Hematopoietic Stem Cell Transplant (HSCT) in Patients Who Developed VODDays +30 and +100 Post-HSCT

VOD-associated MOD is defined for participants as occurring if the investigator answers "Yes" to the question "Has the participant been diagnosed with VOD associated MOD?" in the electronic case report form (eCRF). The values below are the number of participants who received the answer, "Yes."

Percentage of Participants Who Had Resolution of Veno-Occlusive Disease (VOD) by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

The proportion of participants who had resolution of VOD by Day +180 post-HSCT is reported as a percentage.

Time to Resolution of Veno-Occlusive Disease (VOD) by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

Time to Resolution of VOD is calculated as follows: Time to Resolution of VOD= \[Date of VOD resolution\] - \[Date of VOD diagnosis by investigator\].

Percentage of Participants With Veno-Occlusive Disease (VOD) After Day +30 Post-Hematopoietic Stem Cell Transplant (HSCT) up to Days +100 and +180 Post-HSCTDays +100 and +180 Post-HSCT

The values shown are the number and percentage of participants with VOD after day +30 post-HSCT and on or before Days +100 and +180 post-HSCT. The diagnosis of VOD through Day +100 post-HSCT was made by Endpoint Adjudication Committee (EPAC), and the diagnosis of VOD after Day +100 post-HSCT was based on investigator assessments.

Change in 5-Level EuroQol-5D (EQ-5D-5L) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Adult Participants Age ≥ 16 Years: MobilityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-5L, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 Post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in 5-Level EuroQol-5D (EQ-5D-5L) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Adult Participants Age ≥ 16 Years: Self-CareDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-5L, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 Post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in 5-Level EuroQol-5D (EQ-5D-5L) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Adult Participants Age ≥ 16 Years: ActivityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-5L, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 Post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in 5-Level EuroQol-5D (EQ-5D-5L) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Adult Participants Age ≥ 16 Years: PainDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-5L, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 Post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in 5-Level EuroQol-5D (EQ-5D-5L) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Adult Participants Age ≥ 16 Years: AnxietyDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-5L, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 Post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 4 and ≤ 7 Years: MobilityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 4 and ≤ 7 Years: Self-CareDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 4 and ≤ 7 Years: ActivityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 4 and ≤ 7 Years: PainDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 4 and ≤ 7 Years: AnxietyDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 8 and ≤ 15 Years: MobilityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 8 and ≤ 15 Years: Self-CareDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 8 and ≤ 15 Years: ActivityDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 8 and ≤ 15 Years: PainDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Change in EuroQol-5D for Youth (EQ-5D-Y) Dimensions From Baseline to Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT) for Pediatric Participants Age ≥ 8 and ≤ 15 Years: AnxietyDay +180 Post-HSCT

For each of the five dimensions of mobility, self-care, activity, pain, and anxiety based on the descriptive system of the EQ-5D-Y, self-report version, the numbers and percentages of participants for all categories (the three levels of reported problems and question not completed) at Day +180 post-HSCT was assessed. Each dimension was categorized as follows: Condition improved, if the reported level of problem is lower at the assessment than baseline; condition unchanged, if the reported level of problem remains the same; condition deteriorated, if the reported level of problem is higher at that assessment than at baseline; and unknown, if the reported level of problem is missing either at baseline or at that assessment.

Maximum Plasma Concentration (Cmax) of Defibrotide Prophylaxis During the Prophylaxis PhaseDay +1 and +7 Post-HSCT

Cmax is the maximum defibrotide plasma concentration, obtained directly from the observed data. Cmax is a summary statistic and it is not reported on an hourly basis. If veno-occlusive disease (VOD) occurs, the prophylaxis phase starts on the baseline date and ends on the day before the start date of rescue defibrotide. If VOD does not occur, the prophylaxis phase starts on the baseline date and ends on the date of study completion/early termination.

Area Under the Defibrotide Concentration-Time Curve (AUClast) of Defibrotide Prophylaxis During the Prophylaxis PhaseDay +1 and +7 Post-HSCT

AUClast is the area under the defibrotide concentration-time curve from 0 (pre-dose) to time of last quantifiable defibrotide concentration at time "t". AUClast is a summary statistic and it is not reported on an hourly basis. If veno-occlusive disease (VOD) occurs, the prophylaxis phase starts on the baseline date and ends on the day before the start date of rescue defibrotide. If VOD does not occur, the prophylaxis phase starts on the baseline date and ends on the date of study completion/early termination.

Mean Clearance of Defibrotide Prophylaxis During the Prophylaxis PhaseDay +1 and +7 Post-HSCT

Mean systemic clearance after intravenous dosing. Mean clearance is a summary statistic and it is not reported on an hourly basis. If veno-occlusive disease (VOD) occurs, the prophylaxis phase starts on the baseline date and ends on the day before the start date of rescue defibrotide. If VOD does not occur, the prophylaxis phase starts on the baseline date and ends on the date of study completion/early termination.

Volume of Distribution of Defibrotide Prophylaxis During the Prophylaxis PhaseDay +1 and +7 Post-HSCT

Mean volume of distribution following intravenous dosing. Mean volume of distribution is a summary statistic and it is not reported on an hourly basis.If veno-occlusive disease (VOD) occurs, the prophylaxis phase starts on the baseline date and ends on the day before the start date of rescue defibrotide. If VOD does not occur, the prophylaxis phase starts on the baseline date and ends on the date of study completion/early termination.

Maximum Plasma Concentration (Cmax) of Defibrotide Prophylaxis During the Rescue PhaseDay +14 Post-VOD Treatment

Cmax is the maximum defibrotide plasma concentration, obtained directly from the observed data. Cmax is a summary statistic and it is not reported on an hourly basis. For the subset of participants who developed veno-occlusive disease (VOD) and received rescue defibrotide, the rescue treatment phase begins on the start date of rescue defibrotide and ends on the date of study completion/early termination.

Area Under the Defibrotide Concentration-Time Curve (AUClast) of Defibrotide Prophylaxis During the Rescue PhaseDay +14 Post-VOD Treatment

AUClast is the area under the defibrotide concentration-time curve from 0 (pre-dose) to time of last quantifiable defibrotide concentration at time "t". AUClast is a summary statistic and it is not reported on an hourly basis. For the subset of participants who developed veno-occlusive disease (VOD) and received rescue defibrotide, the rescue treatment phase begins on the start date of rescue defibrotide and ends on the date of study completion/early termination.

Volume of Distribution of Defibrotide Prophylaxis During the Rescue PhaseDay +14 Post-VOD Treatment

Mean volume of distribution following intravenous dosing. Mean volume of distribution is a summary statistic and it is not reported on an hourly basis. For the subset of participants who developed veno-occlusive disease (VOD) and received rescue defibrotide, the rescue treatment phase begins on the start date of rescue defibrotide and ends on the date of study completion/early termination.

Percentage of Participants With Grades 2, 3, and 4 Acute Graft-Versus-Host-Disease (GvHD) by Days +30, +100, and +180 Post-Hematopoietic Stem Cell Transplant (HSCT) in the Prophylaxis PhaseDays +30, +100, and +180 Post-HSCT

The number and percentage of participants with Grade 2-4 acute GvHD in the prophylaxis phase. Grade 2 is defined as Skin stage = 3, or Liver stage = 1, or GI stage = 1. Grade 3 is defined as Skin stage = 3, or Liver stage = 2-3, or GI stage = 2-4. Grade 4 is defined as a Skin stage = 4, or Liver stage = 4, or GI stage = 2-4.

Percentage of Participants With Grades 2, 3, and 4 Acute Graft-Versus-Host-Disease (GvHD) by Days +30, +100, and +180 Post-Hematopoietic Stem Cell Transplant (HSCT) in the Rescue PhaseDays +30, +100, and +180 Post-HSCT

The number and percentage of participants with Grade 2-4 acute GvHD in the rescue phase. Grade 2 is defined as Skin stage = 3, or Liver stage = 1, or GI stage = 1. Grade 3 is defined as Skin stage = 3, or Liver stage = 2-3, or GI stage = 2-4. Grade 4 is defined as a Skin stage = 4, or Liver stage = 4, or GI stage = 2-4.

Percentage of Participants With Chronic Graft-Versus-Host-Disease (GvHD) by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

The values shown are the number and percentages of participants who developed chronic GvHD by Day +180 post-HSCT in the prophylaxis phase and rescue phase.

Number of Participants With Graft Failure During the Prophylaxis Phase and Rescue PhaseDay +180 Post-HSCT

Graft failure is defined as participants that after hematopoietic stem cell transplant (HSCT) never reached an absolute neutrophil count \>0.5 x 10\^9/L that is maintained for three consecutive days or a platelet count \>20 x 10\^9/L without a platelet transfusion in the preceding seven days. If veno-occlusive disease (VOD) occurs, the prophylaxis phase starts on the baseline date and ends on the day before the start date of rescue defibrotide. If VOD does not occur, the prophylaxis phase starts on the baseline date and ends on the date of study completion/early termination. For the subset of participants who developed VOD and received rescue defibrotide, the rescue treatment phase begins on the start date of rescue defibrotide and ends on the date of study completion/early termination.

Number of Participants With Neutrophil Engraftment by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

The date of neutrophil engraftment was recorded on the electronic case report form (eCRF) and is defined as the first date after HSCT of an absolute neutrophil count \>0.5 x 10\^9/L that is maintained for three consecutive days. The definition of "absolute neutrophil count" includes both segmented neutrophils and "bands," immature neutrophils. The number of participants with neutrophil engraftment was assessed.

Number of Participants With Platelet Engraftment by Day +180 Post-Hematopoietic Stem Cell Transplant (HSCT)Day +180 Post-HSCT

The date of platelet engraftment was recorded on the electronic case report form (eCRF) and is defined as the first date after HSCT of a platelet count \>20 x 10\^9/L without a platelet transfusion in the preceding seven days. The number of participants with platelet engraftment was assessed.

Trial Locations

Locations (114)

Osaka City University Hospital

🇯🇵

Osaka, Japan

Medical Hospital Tokyo Medical and Dental University

🇯🇵

Tokyo, Japan

Severance Hospital at Yonsei University Health System

🇰🇷

Seoul, Korea, Republic of

The Catholic University of Korea Seoul St. Mary's Hospital

🇰🇷

Seoul, Korea, Republic of

Alfred I Dupont Hospital For Children

🇺🇸

Wilmington, Delaware, United States

Johns Hopkins All Children's Hospital

🇺🇸

Saint Petersburg, Florida, United States

Cliniques Universitaires Saint-Luc

🇧🇪

Bruxelles, Belgium

UZ Gent

🇧🇪

Gent, Belgium

Children's Hospital of Wisconsin

🇺🇸

Milwaukee, Wisconsin, United States

Hôpital Saint Antoine

🇫🇷

Paris, France

Royal Adelaide Hospital

🇦🇺

Adelaide, South Australia, Australia

UZ Leuven Gasthuisberg

🇧🇪

Leuven, Belgium

UZ Leuven

🇧🇪

Leuven, Belgium

Institut Paoli Calmettes

🇫🇷

Marseille, France

Universitätsklinikum Münster

🇩🇪

Münster, Nordrhein-Westfalen, Germany

Universitätsklinikum Carl Gustav Carus an der TU Dresden

🇩🇪

Dresden, Sachsen, Germany

Universitätsklinikum Leipzig

🇩🇪

Leipzig, Sachsen, Germany

Chaim Sheba Medical Center

🇮🇱

Ramat Gan, Israel

Schneider Children Medical Center of Israel

🇮🇱

Petaẖ Tiqwa, Israel

Tel Aviv Sourasky Medical Center

🇮🇱

Tel Aviv, Israel

11. Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona-Umberto I G M Lancisi G Salesi

🇮🇹

Ancona, Italy

Azienda Ospedaliero - Universitaria

🇮🇹

Catania, Italy

Azienda Ospedaliera Universitaria Careggi

🇮🇹

Firenze, Italy

Ospedale Pediatrico Bambino Gesù

🇮🇹

Roma, Italy

AORMN Marche Nord

🇮🇹

Pesaro, Italy

Anjo Kosei Hospital

🇯🇵

Anjo, Japan

Kobe University Hospital

🇯🇵

Hyōgo, Japan

Fondazione Policlinico Universitario A Gemelli

🇮🇹

Roma, Italy

Hokkaido University Hospital

🇯🇵

Sapporo, Japan

Erciyes University Medical Faculty

🇹🇷

Kayseri, Talas, Turkey

Medicana International Ankara Hospital

🇹🇷

Ankara, Turkey

Samsung Medical Center

🇰🇷

Seoul, Korea, Republic of

Toranomon Hospital

🇯🇵

Tokyo, Japan

Seoul National University Hospital

🇰🇷

Seoul, Korea, Republic of

Auckland City Hospital

🇳🇿

Auckland, New Zealand

Hospital Universitario Germans Trias i Pujol

🇪🇸

Badalona, Barcelona, Spain

Hospital Universitario Vall d Hebron

🇪🇸

Barcelona, Spain

Hospital Universitario Reina Sofia

🇪🇸

Cordoba, Spain

Hospital Sant Joan de Deu - PIN

🇪🇸

Esplugues de Llobregat, Spain

Hospital Infantil Universitario Niño Jesus

🇪🇸

Madrid, Spain

Beatson West of Scotland Cancer Centre

🇬🇧

Glasgow, United Kingdom

Children's Hospital Los Angeles

🇺🇸

Los Angeles, California, United States

University of California San Francisco

🇺🇸

San Francisco, California, United States

Children's Healthcare of Atlanta

🇺🇸

Atlanta, Georgia, United States

Rady Childrens Hospital San Diego

🇺🇸

San Diego, California, United States

Ann and Robert H Lurie Childrens Hospital of Chicago

🇺🇸

Chicago, Illinois, United States

Dana Farber Cancer Institute

🇺🇸

Boston, Massachusetts, United States

University Hospital Case Medical Center

🇺🇸

Cleveland, Ohio, United States

Nicklaus Childrens Hospital

🇺🇸

Miami, Florida, United States

Duke University Medical Center

🇺🇸

Durham, North Carolina, United States

Cleveland Clinic

🇺🇸

Cleveland, Ohio, United States

Children's Hospital of Philadelphia

🇺🇸

Philadelphia, Pennsylvania, United States

Children's Medical Center Dallas

🇺🇸

Dallas, Texas, United States

MD Anderson Cancer Center

🇺🇸

Houston, Texas, United States

Primary Children's Hospital

🇺🇸

Salt Lake City, Utah, United States

Children's Hospital of Alabama

🇺🇸

Birmingham, Alabama, United States

Phoenix Children's Hospital

🇺🇸

Phoenix, Arizona, United States

Children's Hospital of Michigan

🇺🇸

Detroit, Michigan, United States

Stanford University

🇺🇸

Palo Alto, California, United States

Children's Hospital at Montefiore

🇺🇸

Bronx, New York, United States

Tufts Floating Hospital for Children

🇺🇸

Boston, Massachusetts, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

Children's Mercy Hospital

🇺🇸

Kansas City, Missouri, United States

Memorial Sloan Kettering Cancer Center

🇺🇸

New York, New York, United States

Royal Children's Hospital Melbourne

🇦🇺

Melbourne, Victoria, Australia

Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Sainte Justine Hospital

🇨🇦

Montreal, Quebec, Canada

Penn State Milton S Hershey Medical Center

🇺🇸

Hershey, Pennsylvania, United States

Doernbecher Children's Hospital

🇺🇸

Portland, Oregon, United States

Medical University of South Carolina - PPDS

🇺🇸

Charleston, South Carolina, United States

Cook Childrens Hospital

🇺🇸

Fort Worth, Texas, United States

Texas Childrens Hospital

🇺🇸

Houston, Texas, United States

Centre Hospitalier Universitaire du Sart Tilman

🇧🇪

Liege, Belgium

Alberta Children's Hospital

🇨🇦

Calgary, Alberta, Canada

CHU de Poitiers

🇫🇷

Poitiers, France

Klinikum Frankfurt Oder GmbH

🇩🇪

Frankfurt (Oder), Brandenburg, Germany

Universitätsklinikum der RWTH Aachen

🇩🇪

Aachen, Nordrhein-Westfalen, Germany

Rambam Health Care Campus

🇮🇱

Haifa, Israel

Universitätsklinikum Hamburg Eppendorf

🇩🇪

Hamburg, Germany

Rambam Health Corporation

🇮🇱

Haifa, Israel

Hadassah Ein Kerem Hospital

🇮🇱

Jerusalem, Israel

Hamanomachi Hospital

🇯🇵

Fukuoka, Japan

Fukushima Medical University Hospital

🇯🇵

Fukushima, Japan

Hyogo College of Medicine

🇯🇵

Nishinomiya, Japan

Tokyo Metropolitan Cancer and Infectious Diseases Center Komagome Hospital

🇯🇵

Tokyo, Japan

Asan Medical Center

🇰🇷

Seoul, Korea, Republic of

Hospital Universitario Ramon y Cajal

🇪🇸

Madrid, Spain

Hospital Regional Universitario de Malaga Hospital General

🇪🇸

Malaga, Spain

Akdeniz University Medical Faculty Department of Pediatrics

🇹🇷

Antalya, Konyaalti, Turkey

St. James University Hospital

🇬🇧

Leeds, United Kingdom

Kings College Hospital

🇬🇧

London, United Kingdom

Medical Park Antalya Hospital

🇹🇷

Antalya, Turkey

Birmingham Children's Hospital

🇬🇧

Birmingham, United Kingdom

Ege Universitesi Tip Fakultesi

🇹🇷

Bornova, Turkey

Acibadem Universitesi Tip Fakultesi Atakent Hastanesi

🇹🇷

Istanbul, Turkey

Acibadem Adana Hospital

🇹🇷

Seyhan, Turkey

Royal Hospital for Children

🇬🇧

Glasgow, United Kingdom

Great Ormond Street Hospital

🇬🇧

London, United Kingdom

Hospital Universitario de Salamanca

🇪🇸

Salamanca, Spain

Hospital General Universitario Morales Meseguer

🇪🇸

Murcia, Spain

Hospital Universitario La Paz

🇪🇸

Madrid, Spain

Hospital Universitario Virgen del Rocio

🇪🇸

Sevilla, Spain

Hopital Jean Minjoz

🇫🇷

Besançon, France

Colorado Children's Hospital

🇺🇸

Aurora, Colorado, United States

University of Arizona Cancer Center

🇺🇸

Tucson, Arizona, United States

Vanderbilt Ingram Cancer Center

🇺🇸

Nashville, Tennessee, United States

Weill Cornell Medical College

🇺🇸

New York, New York, United States

Fred Hutchinson Cancer Research Center

🇺🇸

Seattle, Washington, United States

Institut Universitaire du Cancer de Toulouse - Oncopôle

🇫🇷

Toulouse, France

Klinikum der Universitat Regensburg

🇩🇪

Regensburg, Germany

National Hospital Organization Kumamoto Medical Center

🇯🇵

Kumamoto, Japan

Kanagawa Children's Medical Center

🇯🇵

Kanagawa, Japan

Japanese Red Cross Nagoya Daiichi Hospital

🇯🇵

Nagoya, Japan

Osaka International Cancer Institute

🇯🇵

Osaka, Japan

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