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Safety, Tolerability and Pharmacodynamic Effect of Fazirsiran (TAK-999, ARO-AAT)

Phase 2
Completed
Conditions
Alpha 1-Antitrypsin Deficiency
Interventions
Drug: Fazisiran Injection
Other: Placebo
Registration Number
NCT03945292
Lead Sponsor
Arrowhead Pharmaceuticals
Brief Summary

The purpose of AROAAT2001 (SEQUOIA) is to evaluate the safety, efficacy and tolerability of multiple doses of the investigational product, Fazirsiran Injection, administered subcutaneously to participants with alpha-1 antitrypsin deficiency (AATD).

Detailed Description

Participants will be enrolled to receive multiple subcutaneous injections of Fazirsiran Injection (also referred to as TAK-999 Injection or ARO-AAT Injection) or placebo. Eligible participants will require a pre-dose biopsy completed as part of the study within the screening window. However, any participant with a biopsy result within 1 year of screening showing no fibrosis does not require a pre-dose biopsy. Only participants who have liver fibrosis will undergo a post-dose biopsy and may continue treatment in an open-label phase.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
40
Inclusion Criteria
  • Diagnosis of AATD
  • Liver biopsy at Screening indicating liver fibrosis (score less than F4); a patient with no fibrosis may participate based on a previous biopsy conducted within one year
  • Women of childbearing potential must have a negative pregnancy test, cannot be breastfeeding, and must be willing to use contraception
  • Willing to provide written informed consent and to comply with study requirements
  • Non-smoker for at least 1 year
  • No abnormal finding of clinical relevance at Screening
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Exclusion Criteria
  • Clinically significant health concerns other than AATD
  • Previous diagnosis or diagnosis at Screening of definitive liver cirrhosis
  • Previous lung or liver transplant due to AATD
  • Regular use of alcohol within one month prior to Screening
  • Use of an investigational agent or device within 30 days prior to dosing or current participation in an investigational study involving therapeutic intervention
  • Use of illicit drugs within 1 year prior to Screening

NOTE: additional inclusion/exclusion criteria may apply, per protocol

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Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Fazirsiran 25 mg DB/200 mg OLFazisiran InjectionDouble-blind (DB) Period: Participants with no fibrosis: Administered on Day 1 and Week 4. Participants with fibrosis: Administered on Day 1, Week 4, and Week 16, then every 12 weeks up to 18 total doses. Open-label (OL) Period: Participants with fibrosis at Screening who received double-blind (DB) fazirsiran 25 mg and who completed the post-dose liver biopsy at Week 48 (or Week 72 or Week 96) entered the open-label phase and received fazirsiran 200 mg every 12 weeks for the duration of the study.
Fazirsiran 100 mg DB/200 mg OLFazisiran InjectionDB Period: Participants with no fibrosis: Fazirsiran 100 mg administered on Day 1 and Week 4. Participants with fibrosis: Fazirsiran 100 mg administered on Day 1, Week 4, and Week 16, then every 12 weeks up to 18 total doses. OL Period: Participants with fibrosis at Screening who received double-blind (DB) fazirsiran 100 mg and who completed the post-dose liver biopsy at Week 48 (or Week 72 or Week 96) entered the open-label phase and received fazirsiran 200 mg every 12 weeks for the duration of the study.
Fazirsiran 200 mg DB/200 mg OLFazisiran InjectionDB Period: Participants with no fibrosis: Fazirsiran 200 mg administered on Day 1 and Week 4. Participants with fibrosis: Fazirsiran 200 mg administered on Day 1, Week 4, and Week 16, then every 12 weeks up to 18 total doses. OL Period: Participants with fibrosis at Screening who received double-blind (DB) fazirsiran 200 mg and who completed the post-dose liver biopsy at Week 48 (or Week 72 or Week 96) entered the open-label phase and received fazirsiran 200 mg every 12 weeks for the duration of the study
Placebo DB / Fazirsiran 200 mg OLFazisiran InjectionDB Period: Participants with no fibrosis: Placebo administered on Day 1 and Week 4. Participants with fibrosis: Placebo administered on Day 1, Week 4, and Week 16, then every 12 weeks up to 18 total doses. OL Period: Participants with fibrosis at Screening who received double-blind (DB) placebo and who completed the post-dose liver biopsy at Week 48 (or Week 72 or Week 96) entered the open-label phase and received fazirsiran 200 mg every 12 weeks for the duration of the study.
Placebo DB / Fazirsiran 200 mg OLPlaceboDB Period: Participants with no fibrosis: Placebo administered on Day 1 and Week 4. Participants with fibrosis: Placebo administered on Day 1, Week 4, and Week 16, then every 12 weeks up to 18 total doses. OL Period: Participants with fibrosis at Screening who received double-blind (DB) placebo and who completed the post-dose liver biopsy at Week 48 (or Week 72 or Week 96) entered the open-label phase and received fazirsiran 200 mg every 12 weeks for the duration of the study.
Primary Outcome Measures
NameTimeMethod
Percent Change From Baseline in Serum Z-Alpha-1 Antitrypsin (Z-AAT) at Week 16Baseline, Week 16 (+/- 2 weeks)
Secondary Outcome Measures
NameTimeMethod
Number of Participants With Treatment-Emergent Adverse Events (TEAEs) in the Double-Blind PhaseDouble Blind Phase (up to Week 48): dose administration through end of study (EOS) or Early Termination or first dose of open-label phase fazirsiran.

An adverse event (AE) is any untoward medical occurrence, which does not necessarily have to have a causal relationship with this treatment. A serious adverse event (SAE) is an AE that: results in death; is life-threatening; requires inpatient hospitalization or prolongation of an existing hospitalization; results in persistent or significant disability/incapacity; is a congenital anomaly/birth defect; is a medically important event or reaction. TEAEs/TESAEs are defined as those AEs that first occurred or worsened in severity following dose administration through end of study (EOS) or Early Termination or first dose of open-label phase fazirsiran.

Number of Participants With Treatment-Emergent Adverse Events (TEAEs) in the Open-Label PhaseFrom dose administration of the first dose of open-label phase fazirsiran through EOS or Early Termination (up to Week 196).

An adverse event (AE) is any untoward medical occurrence, which does not necessarily have to have a causal relationship with this treatment. A serious adverse event (SAE) is an AE that: results in death; is life-threatening; requires inpatient hospitalization or prolongation of an existing hospitalization; results in persistent or significant disability/incapacity; is a congenital anomaly/birth defect; is a medically important event or reaction. TEAEs/TESAEs are defined as those AEs that first occurred or worsened in severity following dose administration through end of study (EOS) or Early Termination or first dose of open-label phase fazirsiran.

Absolute Change From Baseline in Total Liver Z-AAT (Insoluble + Soluble) Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Percent Change From Baseline in Total Liver Z-AAT (Insoluble + Soluble) Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Absolute Change From Baseline in Liver Z-AAT Soluble Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Percent Change From Baseline in Liver Z-AAT Soluble Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Absolute Change From Baseline in Liver Z-AAT Insoluble Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Percent Change From Baseline in Liver Z-AAT Insoluble Protein at Post-dose Biopsy for Participants With FibrosisBaseline, Week 48 (+/- 2 weeks), or Week 72 (+/- 4 weeks), or Week 96 (+/- 4 weeks)

Post-dose biopsy includes all post-dose biopsy collected at Week 48 or Week 72 or Week 96.

Absolute Change From Baseline in Liver Function Tests: Alanine Aminotransferase (ALT) at Week 16 and Over Time Through End of Study (EOS)Baseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: ALT at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Aspartate Aminotransferase (AST) at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: AST at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Alkaline Phosphatase (ALP) at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: ALP at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Gamma Glutamyl Transferase (GGT) at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124,136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: GGT at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Total Bilirubin at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124,136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: Total Bilirubin at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Direct Bilirubin at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: Direct Bilirubin at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change From Baseline in Liver Function Tests: Prothrombin International Normalized Ratio at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change From Baseline in Liver Function Tests: Prothrombin International Normalized Ratio at Week 16 and Over Time Through EOSBaseline, Week 16, Week 16 + 24 hours (H), Weeks 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Absolute Change in Serum Z-AAT Over Time Through EOSBaseline, Weeks 2, 4, 6, 16, 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Percent Change in Serum Z-AAT Over Time Through EOSBaseline, Weeks 2, 4, 6, 16, 28, 40, 48, 52, 64, 72, 76, 88, 96, 100, 112, 124, 136, 148, 160, Early Termination (up to 196 weeks), EOS (up to 208 weeks)

PDLB=post-dose liver biopsy

Pharmacokinetics (PK): ARO-AAT Plasma Concentration Summary for the Double-Blind PhaseFazirsiran participants without fibrosis: Pre-dose, 1 hour, 2 hour, 24 hours post-dose on Day 1 (+/- 1 day). Fazirsiran participants with fibrosis: Pre-dose, 1 hour, 2 hours, 24 hours post-dose on Day 1 and Week 16 (+/- 1 day).
Number of Participants Positive for Anti-Drug Antibodies to FazirsiranBaseline, Weeks 4, 16, 28, 40, 48, 52, 64, 76, 88, 96, 100, 112, 124, 136, 148 or Early Termination (up to 148 weeks)

PDLB=post-dose liver biopsy

Percentage of Participants With Shifts From Baseline in METAVIR Fibrosis Stage at Post-Dose Biopsy for Participants With FibrosisBaseline, Post-dose at Weeks 48 (+/- 2 weeks) or Week 72 (+/- 4 weeks) or Week 96 (+/- 4 weeks)

The METAVIR scoring system is a system used to assess the extent of inflammation and fibrosis by histopathological evaluation in a liver biopsy. The stage represents the amount of fibrosis or scarring: 0= no fibrosis; 1=portal fibrosis without septa; 2=portal fibrosis with few septa; 3=numerous septa without cirrhosis; 4=cirrhosis. A higher score indicates a worse condition.

Trial Locations

Locations (21)

UCLA David Geffen School of Medicine, Center for Health Sciences

🇺🇸

Los Angeles, California, United States

University of Iowa Hospitals and Clinics

🇺🇸

Iowa City, Iowa, United States

University of California San Diego Altman Clinical and Translational Research Institute

🇺🇸

La Jolla, California, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

University of Alabama at Birmingham Medical Center

🇺🇸

Birmingham, Alabama, United States

Mayo Clinic Arizona

🇺🇸

Phoenix, Arizona, United States

Vanderbilt University Medical Center

🇺🇸

Nashville, Tennessee, United States

UCSF Medical Center Benioff Children's Hospital

🇺🇸

San Francisco, California, United States

University of Utah Hospital

🇺🇸

Salt Lake City, Utah, United States

Stanford Health Care

🇺🇸

Stanford, California, United States

University of Florida Hepatology Research at CTRB

🇺🇸

Gainesville, Florida, United States

SSM-Health Cardinal Glennon Children's Hospital

🇺🇸

Saint Louis, Missouri, United States

Indiana University Health University Hospital

🇺🇸

Indianapolis, Indiana, United States

Leiden University Medical Center

🇳🇱

Leiden, Netherlands

Universitatsklinikum Aachen, Anstalt des offentlich

🇩🇪

Aachen, Germany

Fondazione IRCCS Policlinico S. Matteo

🇮🇹

Pavia, Italy

Hospital Universitari Vall d'Hebron

🇪🇸

Barcelona, Spain

Medical University of South Carolina (MUSC)

🇺🇸

Charleston, South Carolina, United States

University of California Davis Medical Center

🇺🇸

Sacramento, California, United States

Hospital Central Do Funchal (Hospital Nelio Mendoca)

🇵🇹

Funchal, Portugal

Baylor College of Medicine

🇺🇸

Houston, Texas, United States

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