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Pentostatin for High Risk and Refractory Chronic Graft Versus Host Disease in Children

Phase 2
Completed
Conditions
Graft vs Host Disease
Registration Number
NCT00144430
Lead Sponsor
Ann & Robert H Lurie Children's Hospital of Chicago
Brief Summary

This is a multicenter trial through the Pediatric Blood and Marrow Transplant Consortium.

The Primary hypothesis of this study is that because of its effect as a potent immunosuppressive agent targeting lymphocytes, pentostatin will show a sustained response in pediatric subjects with severe chronic GVHD. Secondary hypotheses include that the infection and toxicity rate of pentostatin in this setting will be acceptable given its lack of severe myelosuppression, and subjects with refractory chronic GVHD will have significant QOL impairment and symptomatology. These may change as subjects are being treated for their chronic GVHD with pentostatin.

Detailed Description

To participate in this study, subjects must have diagnosed chronic Graft versus Host Disease that is refractory to therapy or that is considered high risk (i.e. low platelet count, progressive onset and greater than 50% of body surface area affected). Subjects must have not failed more than 2 immunosuppressive regimens in order to be considered for this trial. Eligible subjects will receive intravenous pentostatin every 2 weeks for 24 weeks. If the subject has had a complete response, the therapy will end at 24 weeks. If the subject has had a partial or mixed response or stable disease, they will continue on study receiving pentostatin for 52 weeks.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
60
Inclusion Criteria

Not provided

Exclusion Criteria
  • More than two previous regimens to treat chronic GVHD. A regimen for the purpose of this study is defined as an adequate trial of an immunosuppressive or immunosuppressive combination (patient was given drug or drugs for 3 months unless there was clear progression during regimen).
  • Calculated Cr. Clearance<30 ml/min/1.73m2
  • Active infection not responding to oral or IV antibiotics.
  • Subjects and families unwilling to firmly commit to return for follow-up doses and appointments.
  • Use of any investigational agent in the past 30 days (this does not include the use of licensed agents for indications not listed in the package insert).
  • Pregnancy or nursing mother; Females of child-bearing potential and sexually active males should use effective contraception while on study.
  • Active veno-occlusive disease of the liver.
  • Bronchiolitis obliterans (defined for the purpose of this study by respiratory symptoms such as shortness of breath or cough and FEV1<50%).
  • Karnofsky performance score less than 40 (or Lansky performance less than 40 in subjects under 16 years of age).

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Primary Outcome Measures
NameTimeMethod
To estimate the response rate (CR and PR) of pentostatin when used to treat refractory-chronic GVHD in children.To end of study
Secondary Outcome Measures
NameTimeMethod
To gather initial efficacy and safety data in high-risk untreated chronic GVHD in children.To end of study
To evaluate toxicities of pentostatin when used to treat chronic GVHD in children.To end of study
To evaluate quality of life (QOL) and symptoms at diagnosis and after therapy with pentostatin in pediatric patients with refractory chronic GVHD.To end of study

Trial Locations

Locations (25)

Loma Linda University Medical Center

🇺🇸

Loma Linda, California, United States

Columbus Children's Hospital

🇺🇸

Columbus, Ohio, United States

Riley Hospital for Children

🇺🇸

Indianapolis, Indiana, United States

Children's Hospital of Philadelphia

🇺🇸

Philadelphia, Pennsylvania, United States

Columbia Presbyterian Medical Center

🇺🇸

New York, New York, United States

Cook Children's Medical Center

🇺🇸

Fort Worth, Texas, United States

St. Louis University

🇺🇸

St. Louis, Missouri, United States

DeVos Children's Hospital

🇺🇸

Grand Rapids, Michigan, United States

Children's Mercy Hospital

🇺🇸

Kansas City, Missouri, United States

University of Utah

🇺🇸

Salt Lake City, Utah, United States

Southwest Texas Methodist Hospital

🇺🇸

San Antonio, Texas, United States

Pediatric Medical Center for Northern California

🇺🇸

Oakland, California, United States

University of Miami

🇺🇸

Miami, Florida, United States

Children's Healthcare of Atlanta

🇺🇸

Atlanta, Georgia, United States

Nemour's Children's Clinic

🇺🇸

Jacksonville, Florida, United States

John's Hopkins

🇺🇸

Baltimore, Maryland, United States

University of Michigan

🇺🇸

Ann Arbor, Michigan, United States

Children's Memorial Hospital

🇺🇸

Chicago, Illinois, United States

Penn State Milton S. Hershey Medical Center

🇺🇸

Hershey, Pennsylvania, United States

Rainbow Babies and Children's

🇺🇸

Cleveland, Ohio, United States

Victor Aquino, MD

🇺🇸

Dallas, Texas, United States

All Children's Health System

🇺🇸

St. Petersburg, Florida, United States

Hackensack University Medical Center

🇺🇸

Hackensack, New Jersey, United States

LSUHSC

🇺🇸

New Orleans, Louisiana, United States

New York Medical College

🇺🇸

Valhalla, New York, United States

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