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Biomarin Pharmaceutical

🇨🇦Canada
Ownership
-
Established
1997-01-01
Employees
-
Market Cap
$17.2B
Website
http://www.biomarin.com

A Study to Evaluate Long-Term Safety, Tolerability, & Efficacy of BMN 111 in Children With Achondroplasia (ACH)

Phase 2
Active, not recruiting
Conditions
Achondroplasia
Interventions
First Posted Date
2016-03-31
Last Posted Date
2025-01-09
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
30
Registration Number
NCT02724228
Locations
🇺🇸

Children's Hospital & Research Center Oakland, Oakland, California, United States

🇺🇸

Harbor - UCLA Medical Center, Torrance, California, United States

🇺🇸

Ann and Robert H. Lurie Childrens Hospital of Chicago, Chicago, Illinois, United States

and more 6 locations

A Safety, Tolerability, and Efficacy Study of BMN 190 in Pediatric Patients < 18 Years of Age With CLN2 Disease

Phase 2
Completed
Conditions
CLN2 Disease
Batten Disease
Late-Infantile Neuronal Ceroid Lipofuscinosis Type 2
CLN2 Disorder
Jansky-Bielschowsky Disease
Interventions
Biological: BMN 190 recombinant human tripeptidyl peptidase-1 (rhTPP1)
Device: Intracerebroventricular access device
First Posted Date
2016-02-10
Last Posted Date
2025-02-17
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
14
Registration Number
NCT02678689
Locations
🇺🇸

Nationwide Children's Hospital, Columbus, Ohio, United States

🇩🇪

Universitaetsklinikum Hamburg-Eppendorf, Hamburg, Germany

🇮🇹

Children's Hospital Bambino Gesù,IRCCS, Rome, Piazza, Italy

and more 1 locations

Extension Study of Drisapersen in DMD Subjects

Conditions
Duchenne Muscular Dystrophy
First Posted Date
2015-12-22
Last Posted Date
2018-01-24
Lead Sponsor
BioMarin Pharmaceutical
Registration Number
NCT02636686
Locations
🇺🇸

Kennedy Krieger Institute, Baltimore, Maryland, United States

🇦🇷

IMAI Research, Buenos Aires, Argentina

🇦🇺

Royal Children's Hosital, Children's Neuroscience Centre, Parkville, Victoria, Australia

and more 36 locations

Gene Therapy Study in Severe Haemophilia A Patients (270-201)

Phase 1
Completed
Conditions
Severe Haemophilia A
Interventions
First Posted Date
2015-10-15
Last Posted Date
2025-04-10
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
15
Registration Number
NCT02576795
Locations
🇬🇧

Queen Elizabeth Hospital Birmingham, Birmingham, United Kingdom

🇬🇧

Addenbrooke's Hospital, Cambridge, United Kingdom

🇬🇧

St. Thomas' Hospital, London, United Kingdom

and more 2 locations

An Extension Study to Evaluate the Long-Term Efficacy and Safety of BMN 190 in Patients With CLN2 Disease

Phase 1
Completed
Conditions
CLN2 Disease
Batten Disease
CLN2 Disorder
Jansky-Bielschowsky Disease
Late-Infantile Neuronal Ceroid Lipofuscinosis Type 2
First Posted Date
2015-06-30
Last Posted Date
2022-08-24
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
23
Registration Number
NCT02485899
Locations
🇺🇸

Nationwide Children's Hospital, Columbus, Ohio, United States

🇩🇪

Universitaetsklinikum Hamburg-Eppendorf, Hamburg, Germany

🇮🇹

Children's Hospital Bambino Gesù,IRCCS, Rome, Piazza, Italy

and more 1 locations

A Phase 3 Substudy to Evaluate Executive Function in Adults With PKU Who Are Participating in the Phase 3 Study, 165-302

Completed
Conditions
Phenylketonuria
First Posted Date
2015-06-11
Last Posted Date
2020-06-04
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
9
Registration Number
NCT02468570
Locations
🇺🇸

University of Kentucky Medical Center, Lexington, Kentucky, United States

🇺🇸

University of Nebraska Medical Center, Omaha, Nebraska, United States

🇺🇸

University of Oklahoma Health Sciences Center, Oklahoma City, Oklahoma, United States

and more 1 locations

Collection and Storage of Human Biospecimens for Research Into Rare Diseases and Medical Conditions

Conditions
Rare Genetic Disorders
First Posted Date
2015-02-18
Last Posted Date
2015-02-18
Lead Sponsor
BioMarin Pharmaceutical
Registration Number
NCT02365376
Locations
🇺🇸

Lurie Children's Hospital of Chicago, Chicago, Illinois, United States

Open Label, Extension Study of PRO044 in Duchenne Muscular Dystrophy (DMD)

Phase 2
Terminated
Conditions
Duchenne Muscular Dystrophy
Interventions
First Posted Date
2015-01-01
Last Posted Date
2017-12-08
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
15
Registration Number
NCT02329769
Locations
🇧🇪

UZ Leuven, Leuven, Belgium

🇮🇹

S.Anna Hospital, Ferrara, Italy

🇮🇹

Policlinico Universitario Agostino Gemelli, Roma, Italy

and more 2 locations

A Multicenter, Multinational, Observational Morquio A Registry Study (MARS)

Completed
Conditions
Mucopolysaccharidosis IV Type A
MPS IVA
Morquio A Syndrome
First Posted Date
2014-11-19
Last Posted Date
2024-03-05
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
418
Registration Number
NCT02294877
Locations
🇺🇸

Phoenix Children's Hospital, Phoenix, Arizona, United States

🇺🇸

Arkansas Children's Hospital, Little Rock, Arkansas, United States

🇺🇸

Children's Hospital of Los Angeles, Los Angeles, California, United States

and more 76 locations

A Prospective, Noninterventional, Observational Study of Late-Onset Pompe Disease

Terminated
Conditions
Late-onset Pompe Patients Untreated or Treated With rhGAA
First Posted Date
2014-08-20
Last Posted Date
2016-10-31
Lead Sponsor
BioMarin Pharmaceutical
Target Recruit Count
30
Registration Number
NCT02221362
Locations
🇦🇺

Westmead Hospital, Dept. of Genetic Medicine, Westmead, New South Wales, Australia

🇦🇺

Women's and Children's Hospital, Adelaide, South Australia, Australia

🇦🇺

Monash Medical Centre, Clayton, Victoria, Australia

and more 12 locations
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