MedPath

A Study Evaluating the Long Term Safety and Efficacy of VX-659 Combination Therapy

Phase 3
Terminated
Conditions
Cystic Fibrosis
Interventions
Registration Number
NCT03447262
Lead Sponsor
Vertex Pharmaceuticals Incorporated
Brief Summary

This study will evaluate the long-term safety and tolerability of VX-659 in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are homozygous or heterozygous for the F508del mutation.

Detailed Description

Not available

Recruitment & Eligibility

Status
TERMINATED
Sex
All
Target Recruitment
484
Inclusion Criteria
  • Completed study drug treatment in a parent study; or had study drug interruption(s) in a parent study but completed study visits up to the last scheduled visit of the Treatment Period in the parent study.
Exclusion Criteria
  • History of drug intolerance in a parent study that would pose an additional risk to the subject in the opinion of the investigator.
  • Current participation in an investigational drug trial (other than a parent study)

Other protocol defined Inclusion/Exclusion criteria may apply.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
VX-659/TEZ/IVA TCIVAParticipants from parent studies VX17-659-102 (NCT03447249) or VX17-659-103 (NCT03460990) were administered VX-659 240 milligrams (mg) once daily (qd)/TEZ 100 mg qd/IVA 150 mg every 12 hours (q12h) in the TC treatment period for up to 96 weeks in the current study VX17-659-105.
VX-659/TEZ/IVA TCVX-659/TEZ/IVAParticipants from parent studies VX17-659-102 (NCT03447249) or VX17-659-103 (NCT03460990) were administered VX-659 240 milligrams (mg) once daily (qd)/TEZ 100 mg qd/IVA 150 mg every 12 hours (q12h) in the TC treatment period for up to 96 weeks in the current study VX17-659-105.
Primary Outcome Measures
NameTimeMethod
Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (AEs) and Serious Adverse Events (SAEs)From Day 1 up to 28 Days After Last Dose of Study Drug or to the Completion of Study Participation Date, Whichever Occurs First in the Current Study 659-105 (up to Week 100)
Secondary Outcome Measures
NameTimeMethod
Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1) for Participants From the Parent Study 659-102From Baseline at Week 72 (Study 659-105)

FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration. The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in BMI Z-score for Participants From the Parent Study 659-102 (Participants <=20 Years Old at Parent Study Baseline)From Baseline at Week 60 (Study 659-105)

BMI was defined as weight in kg divided by squared height in meters (m\^2). The z-score is a statistical measure to describe whether a value was above or below the standard. A z-score of 0 is equal to the standard. Lower numbers indicate values lower than the standard and higher numbers indicate values higher than the standard. The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in Body Weight for Participants From the Parent Study 659-103From Baseline at Week 72 (Study 659-105)

The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in ppFEV1 for Participants From the Parent Study 659-103From Baseline at Week 72 (Study 659-105)

FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration. The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in SwCl for Participants From the Parent Study 659-103From Baseline at Week 24 (Study 659-105)

Sweat samples were collected using an approved collection device. The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Number of Participants With at Least One PEx for Participants From the Parent Study 659-102From Baseline up to Week 96 (Study 659-105)

PEx was defined as treatment with new or changed antibiotic therapy (intravenous, inhaled, or oral) for at least 4 sinopulmonary signs/symptoms. The time-to-first-PEx data were planned to be estimated using the Kaplan-Meier (KM) method. However, because way less than 50% of participants had events, median time-to-first event data were not estimable. Instead, the number of participants with at least one PEx event was assessed and reported separately for those in Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and the VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in the parent study 659-102 or/and VX-659/TEZ/IVA in the current study 659-105). Baseline was defined as the parent study baseline except for Placebo - VX-659/TEZ/IVA category, for which the baseline was defined as study 659-105 baseline.

Absolute Change in BMI for Participants From the Parent Study 659-103From Baseline at Week 72 (Study 659-105)

BMI was defined as weight in kg divided by squared height in meters (m\^2). The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Number of Participants With at Least One PEx for Participants From the Parent Study 659-103From Baseline up to Week 96 (Study 659-105)

PEx was defined as treatment with new or changed antibiotic therapy (intravenous, inhaled, or oral) for at least 4 sinopulmonary signs/symptoms. The time-to-first-PEx data were planned to be estimated using the KM method. However, because way less than 50% of participants had events, median time-to-first-event data were not estimable. Instead, the number of participants with at least one PEx event was assessed and reported for all participants from the parent study 659-103, that is combined for those in the TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and the VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in the parent study 659-103 or/and in the current study 659-105). Baseline was defined as the parent study baseline except for TEZ/IVA - VX-659/TEZ/IVA category, for which the baseline was defined as study 659-105 baseline.

Absolute Change in CFQ-R Respiratory Domain Score for Participants From the Parent Study 659-103From Baseline at Week 72 (Study 659-105)

The CFQ-R is a validated participant-reported outcome measuring health-related quality of life for participants with cystic fibrosis. Respiratory domain assessed respiratory symptoms, score range: 0-100; higher scores indicating fewer symptoms and better health-related quality of life. The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Number of Pulmonary Exacerbations (PEx) for Participants From the Parent Study 659-102From Baseline up to Week 96 (Study 659-105)

PEx was defined as treatment with new or changed antibiotic therapy (intravenous, inhaled, or oral) for at least 4 sinopulmonary signs/symptoms. The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in the parent study 659-102 or/and VX-659/TEZ/IVA in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline except for Placebo - VX-659/TEZ/IVA category, for which the baseline was defined as study 659-105 baseline.

Absolute Change in Body Weight for Participants From the Parent Study 659-102From Baseline at Week 72 (Study 659-105)

The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in Sweat Chloride (SwCl) for Participants From the Parent Study 659-102From Baseline at Week 24 (Study 659-105)

Sweat samples were collected using an approved collection device. The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Number of PEx for Participants From the Parent Study 659-103From Baseline up to Week 96 (Study 659-105)

PEx was defined as treatment with new or changed antibiotic therapy (intravenous, inhaled, or oral) for at least 4 sinopulmonary signs/symptoms. The analysis was planned to be reported for overall participants from the parent study 659-103, that is combined for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in the parent study 659-103 or/and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline except for TEZ/IVA - VX-659/TEZ/IVA category, for which the baseline was defined as study 659-105 baseline.

Absolute Change in Body Mass Index (BMI) for Participants From the Parent Study 659-102From Baseline at Week 72 (Study 659-105)

BMI was defined as weight in kilograms (kg) divided by squared height in meters (m\^2). The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in Cystic Fibrosis Questionnaire-Revised (CFQ-R) Respiratory Domain Score for Participants From the Parent Study 659-102From Baseline at Week 72 (Study 659-105)

The CFQ-R is a validated participant-reported outcome measuring health-related quality of life for participants with cystic fibrosis. Respiratory domain assessed respiratory symptoms, score range: 0-100; higher scores indicating fewer symptoms and better health-related quality of life. The analysis was planned to be reported separately for Placebo - VX-659/TEZ/IVA category (participants who received placebo in the parent study 659-102 and VX-659/TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-102 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Absolute Change in BMI Z-score for Participants From The Parent Study 659-103 (Participants <=20 Years Old at Parent Study Baseline)From Baseline at Week 60 (Study 659-105)

BMI was defined as weight in kg divided by squared height in meters (m\^2). The z-score is a statistical measure to describe whether a value was above or below the standard. A z-score of 0 is equal to the standard. Lower numbers indicate values lower than the standard and higher numbers indicate values higher than the standard. The analysis was planned to be reported separately for TEZ/IVA - VX-659/TEZ/IVA category (participants who received TEZ/IVA in the parent study 659-103 and VX-659-TEZ/IVA in the current study 659-105) and VX-659/TEZ/IVA - VX-659/TEZ/IVA category (participants who received VX-659/TEZ/IVA in both the parent study 659-103 and in the current study 659-105) as pre-specified in analysis plan. Baseline was defined as the parent study baseline.

Trial Locations

Locations (100)

Johns Hopkins Hospital

🇺🇸

Baltimore, Maryland, United States

Drexel University College of Medicine / Drexel Adult Cystic Fibrosis Center

🇺🇸

Philadelphia, Pennsylvania, United States

Cork University Hospital

🇮🇪

Cork, Ireland

Boston Children's Hospital

🇺🇸

Boston, Massachusetts, United States

Seattle Children's Hospital

🇺🇸

Seattle, Washington, United States

University of Miami Miller School of Medicine

🇺🇸

Miami, Florida, United States

Nicklaus Children's Hospital

🇺🇸

Miami, Florida, United States

Indiana Clinical Research Center, IU Health University Hospital

🇺🇸

Indianapolis, Indiana, United States

Lady Cilento Children's Hospital

🇦🇺

South Brisbane, Australia

Cincinnati Children's Hospital

🇺🇸

Cincinnati, Ohio, United States

Hospital Universitari Vall d Hebron

🇪🇸

Barcelona, Spain

Hospital Universitari Vall d´Hebron Servicio de Broncoscopia

🇪🇸

Barcelona, Spain

Kinderspital Zuerich

🇨🇭

Zürich, Switzerland

Liverpool Head and Chest Hospital

🇬🇧

Liverpool, United Kingdom

University of Alabama at Birmingham

🇺🇸

Birmingham, Alabama, United States

University of Minnesota

🇺🇸

Minneapolis, Minnesota, United States

Duke University Medical Center

🇺🇸

Durham, North Carolina, United States

Santiago Reyes, M.D.

🇺🇸

Oklahoma City, Oklahoma, United States

Oregon Health & Science University

🇺🇸

Portland, Oregon, United States

Vanderbilt University Medical Center

🇺🇸

Nashville, Tennessee, United States

University of Utah/ Primary Children's Medical Center

🇺🇸

Salt Lake City, Utah, United States

Children's Hospital Colorado

🇺🇸

Aurora, Colorado, United States

Alfred Hospital

🇦🇺

Melbourne, Australia

Stanford University

🇺🇸

Palo Alto, California, United States

Hartford Hospital

🇺🇸

Hartford, Connecticut, United States

Yale New Haven Medical Center

🇺🇸

New Haven, Connecticut, United States

Orlando Health, Inc.- Arnold Palmer Hospital for Children (APH)

🇺🇸

Orlando, Florida, United States

St. Luke's CF Center of Idaho

🇺🇸

Boise, Idaho, United States

Johns Hopkins All Children's Hospital Outpatient Care Center

🇺🇸

Saint Petersburg, Florida, United States

Cystic Fibrosis Center of Chicago

🇺🇸

Glenview, Illinois, United States

Advocate Children's Hospital - Park Ridge / North Suburban Pulmonary and Critical Care Consultants

🇺🇸

Niles, Illinois, United States

University of Kentucky

🇺🇸

Lexington, Kentucky, United States

Kosair Charities Pediatric Clinical Research Unit

🇺🇸

Louisville, Kentucky, United States

The University of Iowa Hospitals and Clinics

🇺🇸

Iowa City, Iowa, United States

Spectrum Health Medical Group Adult Cystic Fibrosis Care Center

🇺🇸

Grand Rapids, Michigan, United States

UMass Memorial Medical Center

🇺🇸

Worcester, Massachusetts, United States

Michigan Medicine

🇺🇸

Ann Arbor, Michigan, United States

University of Mississippi Medical Center

🇺🇸

Jackson, Mississippi, United States

The Children's Mercy Hospital

🇺🇸

Kansas City, Missouri, United States

Rutgers-Robert Wood Johnson Medical School

🇺🇸

New Brunswick, New Jersey, United States

Dartmouth Hitchcock, Manchester

🇺🇸

Manchester, New Hampshire, United States

Washington University School of Medicine/ St. Louis Children's Hospital

🇺🇸

Saint Louis, Missouri, United States

Albany Medical College

🇺🇸

Albany, New York, United States

CF Therapeutics Development Center of Western New York

🇺🇸

Buffalo, New York, United States

Northwell Health, Long Island Jewish Medical Center

🇺🇸

New Hyde Park, New York, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

Clinical Research of Charlotte

🇺🇸

Charlotte, North Carolina, United States

SUNY Upstate Medical University

🇺🇸

Syracuse, New York, United States

Sanford Children's Specialty Clinic

🇺🇸

Sioux Falls, South Dakota, United States

Children's Hospital of Pittsburgh of UPMC

🇺🇸

Pittsburgh, Pennsylvania, United States

Children's Foundation Research Center / Le Bonheur Children's Hospital

🇺🇸

Memphis, Tennessee, United States

University of Tennessee Medical Center- Adult Cystic Fibrosis Clinic

🇺🇸

Knoxville, Tennessee, United States

Cook Children's Medical Center

🇺🇸

Fort Worth, Texas, United States

Texas Children's Hospital

🇺🇸

Houston, Texas, United States

Providence Pediatric Pulmonary & Cystic Fibrosis Clinic

🇺🇸

Spokane, Washington, United States

Institute for Respiratory Health, Sir Charles Gairdner Hospital

🇦🇺

Nedlands, Australia

Royal Adelaide Hospital

🇦🇺

Adelaide, Australia

The Prince Charles Hospital

🇦🇺

Chermside, Australia

John Hunter Hospital & Hunter Medical Research Institute and John Hunter Children's Hospital

🇦🇺

New Lambton, Australia

Telethon Kids Institute

🇦🇺

Perth, Australia

Sydney Children's Hospital

🇦🇺

Randwick, Australia

St. Michael's Hospital

🇨🇦

Toronto, Canada

Stollery Children's Hospital

🇨🇦

Edmonton, Canada

Queen Elizabeth II Health Sciences Center

🇨🇦

Halifax, Canada

Charite Paediatric Pulmonology Department

🇩🇪

Berlin, Germany

Juliane Marie Center, Rigshospitalet

🇩🇰

Copenhagen, Denmark

Medizinische Hochschule Hannover

🇩🇪

Hannover, Germany

Clinic of J.W. Goethe University

🇩🇪

Frankfurt, Germany

Ruhrlandklinik Westdeutsches Lungenzentrum am Klinikum Essen

🇩🇪

Essen, Germany

Universitaetsklinkum Koeln, CF-Studienzentrum

🇩🇪

Koeln, Germany

Mukeviszidose-Zentrum am Universitatsklinikum Jena, Klinik fuer Kinder- und Jugendmedizin

🇩🇪

Jena, Germany

Klinikum Innenstadt, University of Munich

🇩🇪

München, Germany

Beaumont Hospital

🇮🇪

Dublin, Ireland

Universitatsklinikum Schleswig-Holstein, Klinik für Kinder- und Jugendmedizin

🇩🇪

Lubeck, Germany

Pneumologische Praxis Pasing

🇩🇪

Muenchen, Germany

Our Lady's Children's Hospital

🇮🇪

Dublin, Ireland

University Hospital Galway

🇮🇪

Galway, Ireland

University Hospital Limerick

🇮🇪

Limerick, Ireland

St. Vincent's University Hospital

🇮🇪

Dublin, Ireland

Temple Street Children's University Hospital

🇮🇪

Dublin, Ireland

Lady Davis Carmel Medical Center

🇮🇱

Haifa, Israel

Rambam Health Care Campus, Liver Unit

🇮🇱

Haifa, Israel

Pediatrics Hadassah Medical Center

🇮🇱

Jerusalem, Israel

Schneider Children's Medical Center

🇮🇱

Petah Tikva, Israel

Sheba Medical Center

🇮🇱

Tel HaShomer, Israel

Klinika Mukowiscydozy IMD Oddozial Chorob Pluc Szpzoz IM. Dzieci WarszaWY

🇵🇱

Łomianki, Poland

Hospital Universitario 12 de Octubre

🇪🇸

Madrid, Spain

Hospital Universitario Infantil La Paz

🇪🇸

Madrid, Spain

Lindenhofspital - Quartier Bleu

🇨🇭

Bern, Switzerland

Hospital Universitario Virgen del Rocio

🇪🇸

Sevilla, Spain

Parc Tauli Sabadell Hospital Universitari

🇪🇸

Sabadell, Spain

Papworth Hospital NHS Foundation Trust, Papworth Everard

🇬🇧

Cambridge, United Kingdom

St. James University Hospital

🇬🇧

Leeds, United Kingdom

Hospital Universitario y Politecnico La Fe

🇪🇸

Valencia, Spain

Clinical Research Facility, Queen Elizabeth University Hospital

🇬🇧

Glasgow, United Kingdom

Royal Brompton & Harefield NHS Foundation Trust, Royal Brompton Hospital

🇬🇧

London, United Kingdom

Wythenshaw e Hospital

🇬🇧

Manchester, United Kingdom

Wolfson Cystic Fibrosis Unit, City Campus

🇬🇧

Nottingham, United Kingdom

The Newcastle upon Tyne Hospitals NHS Foundation Trust, The Royal Victoria Infirmary

🇬🇧

Newcastle Upon Tyne, United Kingdom

All Wales Adult Cystic Fibrosis Centre, University Hospital Llandough

🇬🇧

Penarth, United Kingdom

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