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Secondary Cancers in Myeloproliferative Neoplasms (MPN-K Study)

Completed
Conditions
Essential Thrombocythemia
Polycythemia Vera
Myelofibrosis
Registration Number
NCT03745378
Lead Sponsor
FROM- Fondazione per la Ricerca Ospedale di Bergamo- ETS
Brief Summary

The incidence of secondary cancer (SC) in patients with myeloproliferative neoplasms (MPN) is high and comparable to that of thrombosis. However, the identification of patient subgroups that might be at increased susceptibility of developing SC has not been systematically addressed. This international case-control study (MPN-K) is aimed to elucidate the prognostic role of JAK2V617F mutation in predicting the occurrence of SC in patients with classical MPN, polycythemia vera (PV), essential thrombocythemia (ET) and myelofibrosis (MF)

Detailed Description

For each recruited case with concomitant diagnosis of myeloproliferative neoplasms (MPN) and secondary cancer each participating center will provide up 3 control patients (1 control for each case could be accepted but the optimal number is 3). Controls are patients with myeloproliferative neoplasms and no history of cancer. Each control will be matched to the paired case for sex, age (+/- 3 years), date of MPN diagnosis (+/- 5 years), and MPN disease duration (+/- 3 years).

Each control is censored at the date of the secondary cancer occurrence in his matched case (index date).

Data will be collected retrospectively from pre-existing medical records and reported by each center on a web-based and validated eCRF developed to record y all study data. In order to maintain patient privacy, all data records will be treated anonymously and no personal data to identify patient will be recorded: patients will be identified in the study by an alphanumeric code.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
1881
Inclusion Criteria
  • Diagnosis of Philadelphia-negative Myeloproliferative Neoplasms (MPN) according to PVSG, 2008 and 2016 WHO criteria, including:
  • Polycythemia Vera (PV)
  • Essential Thrombocythemia (ET)
  • Myelofibrosis (MF), including both primary and secondary MF
  • Diagnosis performed between 1st January 2000 to 31 December 2016
  • Diagnosis of secondary cancer(s) performed concurrently or subsequently the diagnosis of MPN
Exclusion Criteria
  • Diagnosis of cancer occurred before the diagnosis of MPN (PV, ET, MF)

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Number of patients with secondary cancers after diagnosis of Polycythemia Vera (PV), Essential Trombocythemia (ET) and Myelofibrosis (MF)10 year from diagnosis of PV, ET or MF

The ratio of number of patients showing JAK2V617F mutation on the number of patients not exposed to this mutation will be calculated in the group of subjects experiencing second cancer after diagnosis of PV, ET and MF (defined as 'cases') and related (odds ratio) with the ratio of patients exposed on those not exposed to JAK2V617F mutation in the group of subjects with no experience of secondary cancers after diagnosis of PV, ET and MF (this group is defined as 'Control' group)

Secondary Outcome Measures
NameTimeMethod
Number of patients with secondary cancers after diagnosis of Polycythemia Vera (PV), Essential Trombocythemia (ET) and Myelofibrosis (MF) in subgroups of subjects exposed to potential risk factors at diagnosis10 year from diagnosis of PV, ET or MF

Characteristics at diagnosis of patients with PV, ET and MF (including other mutations) with occurrence of second cancers (SC) are decribed and compared with those not experiencing SC after diagnosis of myloproliferative neoplasm; the ratio of number of patients exposed to potential risk factors on the number of subjects not exposed will be calculated in the group cases (as defined for primary outcome measure) and related (odds ratio) with the ratio of patient exposed versus not exposed calculated in the subgroup of control.

Number of patients with secondary cancers after diagnosis of Polycythemia Vera (PV), Essential Trombocythemia (ET) and Myelofibrosis (MF) in the subgroups exposed to treatment10 year from diagnosis of PV, ET or MF

Group of patients exposed and not exposed to different class of treatments for PV, ET and MF are compared and related in the group of cases and control

Trial Locations

Locations (30)

Palacky University and University Hospital Olomouc, Faculty of Medecine

🇨🇿

Olomouc, Czechia

University Hospital RWTH - Department Oncology, Hematology, Hemostaeseology and stem cell transplantation

🇩🇪

Aachen, Germany

Johannes Wesling Academic Medical Center

🇩🇪

Minden, Germany

Meir Medical Center

🇮🇱

Kfar Saba, Israel

Azienda Sanitaria di Asti - A.S.L. AT Ospedale Cardinal Massaia - S.C. Oncologia

🇮🇹

Asti, Italy

ASST- Papa Giovanni XXIII - UOC Ematologia

🇮🇹

Bergamo, Italy

Ospedale S. Orsola - Malpighi - UO Ematologia

🇮🇹

Bologna, Italy

U.O. Emostasi "G. Rodolico" Dipartimento di Scienze Mediche, Chirurgiche e Tecnologiche Avanzate "G.F. Ingrassia" Università degli Studi di Catania

🇮🇹

Catania, Italy

Azienda Ospedaliera S. Croce e Carle di Cuneo- Divisione di Ematologia,

🇮🇹

Cuneo, Italy

AOU Careggi di Firenze CRIMM- Center of Research and Innovation of Myeloproliferative Neoplasms - Department of Experimental and Clinical Medicine, University of Florence

🇮🇹

Firenze, Italy

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Palacky University and University Hospital Olomouc, Faculty of Medecine
🇨🇿Olomouc, Czechia

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