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Pharmacokinetic (PK), Pharmacodynamic (PD) and Tolerability of Osilodrostat in Pediatric Patients With Cushing's Syndrome

Phase 2
Recruiting
Conditions
Cushing Syndrome
Interventions
Registration Number
NCT03708900
Lead Sponsor
RECORDATI GROUP
Brief Summary

Multicenter, open-label, non-comparative study to evaluate the pharmacokinetics, pharmacodynamics, and tolerability of osilodrostat in children and adolescent patients with Cushing's syndrome.

Detailed Description

The period 1 study duration will be 12 weeks. The study will include a screening period of up to 4 weeks prior to Day 0 (baseline) (to allow for an adequate washout period from any medications that may modify cortisol levels). All subjects being treated with osilodrostat at 12 weeks and obtaining benefit from therapy, per investigator judgment, will be offered participation in an optional 9-month extension period, during which assessment of the PD activity and safety/tolerability of osilodrostat will be done. Patients who do not enter the optional extension period will have a safety follow up visit 4 weeks later.

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
12
Inclusion Criteria

Not provided

Exclusion Criteria

Not provided

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
LCI699 (osilodrostat)LCI699Subjects with cushing's syndrome taking LCI699 (osilodrostat)
Primary Outcome Measures
NameTimeMethod
Core Study: Evaluate the pharmacokinetics (PK) of osilodrostat using Pharmacokinetic parameters of osilodrostat up to Week 12 in children and adolescents 2 to less than 18 years of age with Cushing's Syndromeup to Week 12

evaluate the pharmacokinetics (PK) of osilodrostat in children and adolescents of 2 to less than 18 years of age with Cushing's Syndrome

Secondary Outcome Measures
NameTimeMethod
Core Study: Percentage of patients with normal mean urinary free cortisol (mUFC) at week 3, 6, 9 and week 12 (or end of treatment)week 3, 6, 9 and week 12 (or end of treatment)

The assessment in the core period will be done by taking the percentage of patients with normal mUFC at week 6 and week 12 (or end of treatment).

Core Study: Change from baseline in mean urinary free cortisol (mUFC) during the core study periodweek 3, 6, 9 and week 12 (or end of treatment)

The assessment will be done by comparison of change from the baseline in mUFC during core study period on patients

Extension: Efficacy of osilodrostat as measured by mUFC levels up to Month 12up to month 12

The assessment of efficacy of osilodrostat to be measured byproportion of patients with normal mUFC levels at each visit up to 12 months

assessment of the pharmacodynamics, safety and tolerability of osilodrostat.up to 12 months

Change from baseline in height at each visit in extension period

assessment of the pharmacodynamics, safety and tolerability of osilodrostat up to 12 monthsup to 12 months

Change from baseline in weight at each visit in extension period

assessment of the pharmacodynamics, safety and tolerability of osilodrostat.assessment of the pharmacodynamics, safety and tolerability of osilodrostat.up to 12 months

Change from baseline in body mass index at each visit in extension period

Trial Locations

Locations (12)

University of California San Francisco UCSF

🇺🇸

San Francisco, California, United States

National Institute of Child Health and Human Development

🇺🇸

Bethesda, Maryland, United States

UZ Brussel

🇧🇪

Jette, Brussel, Belgium

Hospital Necker Enfants Malades

🇫🇷

Paris, France

Multiprofile Hospital for Active Treatment Sveta Marina EAD

🇧🇬

Varna, Bulgaria

Aziendal Ospedaliero Universitaria Pisana Presidio Ospedale di Cisanello

🇮🇹

Pisa, PI, Italy

Robert Debre Hospital

🇫🇷

Paris, France

CHU Bicetre APHP Paris Saclay

🇫🇷

Paris, France

Ospedale Bambino Gesu

🇮🇹

Roma, Italy

University Clinical Center Ljubljana

🇸🇮

Ljubljana, Slovenia

Alder Hey Childrens NHS Foundation Trust

🇬🇧

Liverpool, United Kingdom

The Royal London Childrens Hospital

🇬🇧

London, United Kingdom

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