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Eisenmenger Quality Enhancement Research Initiative

Completed
Conditions
Pulmonary Arterial Hypertension
Interventions
Other: Subjects with diagnosis of Eisenmenger Syndrome
Registration Number
NCT01623492
Lead Sponsor
Actelion
Brief Summary

Eisenmenger Quality Enhancement Research Initiative (QuERI) is a multi-center, observational, US-based longitudinal program, with enrollment of consecutive Eisenmenger patients who meet enrollment. Patient data will be collected prospectively for three years. Individual physician feedback will be provided on data collected with the purpose of improving the management of patients - quality enhancement research initiative (QuERI) process.

Detailed Description

Approximately 200 male and female adult patients with a history of Eisenmenger will be recruited from approximately 50 cardiology practices over a period of 18 months and will be followed up every six months for the period of three years. Consecutive patients in each practice meeting inclusion and exclusion criteria should be considered for the study. Participating sites will be asked to maintain a screening log to identify which inclusion or exclusion criteria was not met thus excluding them from the study.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
193
Inclusion Criteria
  • Male and female patients
  • Diagnosis of Eisenmenger syndrome based on right heart catheterization data
  • Right to Left intra-cardiac shunting
  • PAH
  • Need for comprehensive management according to guidelines and peer-reviewed evidence
  • Ability and desire to execute the consent for follow up
Exclusion Criteria
  • Poor mental function, drug, or substance (e.g.,alcohol) abuse, or unstable psychiatric illness, which, in the opinion of the investigator, may interfere with optimal participation in the study
  • Prior inclusion in this program

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Arm && Interventions
GroupInterventionDescription
diagnosis of Eisenmenger SyndromeSubjects with diagnosis of Eisenmenger Syndromesubjects with diagnosis of Eisenmenger Syndrome
Primary Outcome Measures
NameTimeMethod
Characterization of the clinical course of patients with Eisenmenger Syndromeup to 3 years

The management of Eisenmenger Syndrome patients over the three year registry period will be compared with established national guidelines. In addition, The Minnesota Living with Heart Failure questionnaire (MLHFQ) will be collected.

Secondary Outcome Measures
NameTimeMethod
Characterization of patients treated with PAH-specific medications to patients untreated with PAH-specific medications.baseline (visit 1) thru end of study (3 years)
Characterization of the demographics of patients with Eisenmenger Syndromebaseline (visit 1) thru end of study (3 years)
Identification of clinical predictors of short-term and long-term outcomes of patients with Eisenmenger Syndrome.baseline (visit 1) thru end of study (3 years)

Trial Locations

Locations (51)

Fletcher Allen Health Care

🇺🇸

Burlington, Vermont, United States

The Pennsylvania State University College of Medicine and The Pennsylvania State Milton S. Hershey Medical Center

🇺🇸

Hershey, Pennsylvania, United States

University of Southern California Adult Congenital Heart Disease Care Program

🇺🇸

Los Angeles, California, United States

University of Maryland School of Medicine

🇺🇸

Baltimore, Maryland, United States

The Cleveland Clinic Adult Congenital Heart Disease Center

🇺🇸

Cleveland, Ohio, United States

Ohio State University Medical Center

🇺🇸

Columbus, Ohio, United States

The Research Institute at Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Temple University Hospital

🇺🇸

Philadelphia, Pennsylvania, United States

Texas Children's Hospital/Baylor College of Medicine

🇺🇸

Houston, Texas, United States

University of Washington

🇺🇸

Seattle, Washington, United States

Children's Heart Center Nevada

🇺🇸

Las Vegas, Nevada, United States

UC Health/University of Cincinnati

🇺🇸

Cincinnati, Ohio, United States

CINCINNATI Children's Hospital Medical Center

🇺🇸

Cincinnati, Ohio, United States

University of Minnesota Physicians Heart Fairview

🇺🇸

Minneapolis, Minnesota, United States

Duke University Medical Center

🇺🇸

Durham, North Carolina, United States

Lucile Packard Children's Hospital

🇺🇸

Palo Alto, California, United States

East Carolina University

🇺🇸

Greenville, North Carolina, United States

Ahmanson / UCLA Adult Congenital Heart Disease Center

🇺🇸

Los Angeles, California, United States

Lenox Hill Hospital

🇺🇸

New York, New York, United States

Berkeley Cardiovascular Medical Group

🇺🇸

Oakland, California, United States

Children's National Medical Center and Washington Hospital Center

🇺🇸

Washington, District of Columbia, United States

Cohen's Children's Medical Center of New York - Adult Congenital Heart Disease Program

🇺🇸

New Hyde Park, New York, United States

The Cardiovascular Group Centra

🇺🇸

Lynchburg, Virginia, United States

Pediatric Cardiology Associates

🇺🇸

Portland, Maine, United States

Columbia University Pulmonary Hypertension Center

🇺🇸

New York, New York, United States

Methodist Lebonheur Healthcare, UT Lebonheur Pediatric Specialists

🇺🇸

Memphis, Tennessee, United States

University of Virginia Health Systems

🇺🇸

Charlottesville, Virginia, United States

Bassett Healthcare Network - Bassett Medical Center

🇺🇸

Cooperstown, New York, United States

Harbor - UCLA Medical Center - Adult Congenital Heart Disease Program - Division of Cardiology

🇺🇸

Torrance, California, United States

Mount Sinai Medical Center

🇺🇸

New York, New York, United States

Medical University of South Carolina

🇺🇸

Charleston, North Carolina, United States

The University of Arkansas for Medical Sciences

🇺🇸

Little Rock, Arkansas, United States

Asheville Cardiology Associates

🇺🇸

Asheville, North Carolina, United States

Rush University Medical Center

🇺🇸

Chicago, Illinois, United States

The University of Kansas Hospital

🇺🇸

Kansas City, Kansas, United States

University of Chicago

🇺🇸

Chicago, Illinois, United States

Providence Sacred Heart Medical Center and Children's Hospital

🇺🇸

Spokane, Washington, United States

Barnes-Jewish Hospital/St. Louis Children's Hospital / Washington University School of Medicine

🇺🇸

Saint Louis, Missouri, United States

Children's Specialty Group PLLC, Children's Hospital of the King's Daughters

🇺🇸

Norfolk, Virginia, United States

Children's Hospital Boston and Brigham and Women's Hospital

🇺🇸

Boston, Massachusetts, United States

Centre for Adult Congenital Heart Disease at California Pacific

🇺🇸

San Francisco, California, United States

University of California, San Francisco

🇺🇸

San Francisco, California, United States

Yale School of Medicine - Adult Congenital Heart Disease Program

🇺🇸

New Haven, Connecticut, United States

University of Louisville, Pediatric Cardiology

🇺🇸

Louisville, Kentucky, United States

University of Colorado Hospital

🇺🇸

Aurora, Colorado, United States

Children's Hospital of Wisconsin, Medical College of Wisconsin Adult Congenital Heart Disease Program

🇺🇸

Milwaukee, Wisconsin, United States

University of Michigan

🇺🇸

Ann Arbor, Michigan, United States

Mid-America Heart Institute / Saint Luke's Hospital / Saint Luke's Cardiovascular Consultants

🇺🇸

Kansas City, Missouri, United States

Oregon Health and Sciences University

🇺🇸

Portland, Oregon, United States

Vanderbilt University Medical Center

🇺🇸

Nashville, Tennessee, United States

Montefiore Medical Center - Moses Division;The University Hospital for Albert Einstein College of Medicine

🇺🇸

Bronx, New York, United States

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