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Long-term Extension of GTX-102 in Angelman Syndrome

Phase 3
Conditions
Angelman Syndrome
Interventions
Registration Number
NCT06415344
Lead Sponsor
Ultragenyx Pharmaceutical Inc
Brief Summary

The primary objective of the study is to evaluate the long-term safety profile of GTX-102 in participants with Angelman Syndrome (AS)

Detailed Description

This study is a phase 3, long term extension (LTE) which is open to participants rolling over from a prior GTX-102 clinical study. The LTE study will evaluate the long-term safety and efficacy of GTX-102 in participants with AS.

Recruitment & Eligibility

Status
ENROLLING_BY_INVITATION
Sex
All
Target Recruitment
75
Inclusion Criteria
  • Signed informed consent from parent(s) or legal guardian(s).
  • Prior participation in a clinical trial with GTX-102; the timing for the roll-over into this study from a prior GTX-102 study is based on the Investigator and Ultragenyx Medical Monitor's approval.
  • From the time of informed consent through the end of the study and for at least 6 months after the final dose of GTX-102, females of childbearing potential who are sexually active must use highly effective contraception or abstinence. Males are able to participate if they agree to remain abstinent (refrain from heterosexual intercourse) or use acceptable contraceptive methods during the study and for at least 3 months after the final dose of GTX-102.
Exclusion Criteria
  • Known hypersensitivity to GTX-102 or its excipients that, in the judgment of the Investigator, places the subject at increased risk for adverse effects.
  • Pregnant or breastfeeding or planning to become pregnant (self or partner) at any time during the study

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
GTX-102GTX-102Participants will receive GTX-102 via intrathecal lumbar puncture (IT LP) on a intrapatient flexible dosing schedule.
Primary Outcome Measures
NameTimeMethod
Frequency, Severity, and Relationship to Investigational Drug of Treatment Emergent Adverse Events (AEs) and Serious Adverse Events (SAEs)5 Years
Secondary Outcome Measures
NameTimeMethod
Change from LTE Month 0 and Pretreatment in the Bayley-4 Raw ScoreMonth 0, 5 Years

Trial Locations

Locations (23)

Corporacio Sanitaria Parc Tauli - Hospital de Sabadell

🇪🇸

Sabadell, Spain

University of California, Los Angeles (UCLA)

🇺🇸

Los Angeles, California, United States

University of California, San Diego - Rady Children's Hospital

🇺🇸

San Diego, California, United States

Rare Disease Research, LLC

🇺🇸

Atlanta, Georgia, United States

Rush University Medical Center

🇺🇸

Chicago, Illinois, United States

Boston Children's Hospital

🇺🇸

Boston, Massachusetts, United States

Weill Cornell Medicine

🇺🇸

New York, New York, United States

Queensland Children's Hospital

🇦🇺

South Brisbane, Queensland, Australia

The Royal Children's Hospital

🇦🇺

Melbourne, Victoria, Australia

MAGIC Clinic Ltd

🇨🇦

Calgary, Alberta, Canada

British Columbia Children's Hospital

🇨🇦

Vancouver, British Columbia, Canada

Childrens Hospital London Health Sciences Centre

🇨🇦

London, Ontario, Canada

Childrens Hospital of Eastern Ontario

🇨🇦

Ottawa, Ontario, Canada

The Research Institute of the McGill University Health Centre

🇨🇦

Montreal, Quebec, Canada

AP-HM - Hopital de la Timone

🇫🇷

Marseille, France

AP-HP Hopital Necker-Enfants Malades

🇫🇷

Paris, France

Universitaetsklinikum Hamburg-Eppendorf

🇩🇪

Hamburg, Germany

Universitaetsklinikum Leipzig

🇩🇪

Leipzig, Germany

Sheba Medical Center

🇮🇱

Ramat Gan, Israel

Hospital Universitario Puerta de Hierro

🇪🇸

Majadahonda, Spain

University of Cambridge

🇬🇧

Cambridge, United Kingdom

Great Ormond Street Hospital for Children

🇬🇧

London, United Kingdom

Oxford University Hospitals NHS Foundation Trust

🇬🇧

Oxford, United Kingdom

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