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A Phase 1/2 Study of VX-670 in Adult Participants With Myotonic Dystrophy 1 (DM1)

Phase 1
Recruiting
Conditions
Myotonic Dystrophy Type 1 (DM1)
Interventions
Drug: Placebo
Registration Number
NCT06185764
Lead Sponsor
Vertex Pharmaceuticals Incorporated
Brief Summary

The purpose of the study is to evaluate the safety, tolerability, pharmacokinetics, and pharmacodynamics of VX-670 at different single and multiple doses in participants with DM1.

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
36
Inclusion Criteria
  • Documented clinical diagnosis of DM1 with age of onset greater than (>) 1 year of age and documented positive genetic test for DM1 in the subject with cytosine thymine guanine (CTG) repeat of at least 100

Key

Exclusion Criteria
  • History of any illness or any clinical condition as pre-specified in the protocol

Other protocol defined Inclusion/Exclusion criteria may apply.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SEQUENTIAL
Arm && Interventions
GroupInterventionDescription
Part A: Single Ascending DoseVX-670Participants will be randomized to receive a single dose of different dose levels of VX-670.
Part A: PlaceboPlaceboParticipants will be randomized to receive single dose of placebo matched to VX-670.
Part B: Single and Multiple Ascending DoseVX-670Participants will be randomized to receive single and multiple doses of different dose levels of VX-670. The dose levels will be determined based on the data from Part A.
Part B: PlaceboPlaceboParticipants will be randomized to receive single or multiple doses of placebo matched to VX-670.
Primary Outcome Measures
NameTimeMethod
Parts A and B: Safety and Tolerability as Assessed by Number of Participants With Adverse Events (AEs)Part A: From Baseline up to Day 42; Part B: From Baseline and up to Day 168
Secondary Outcome Measures
NameTimeMethod
Part B: Area Under the Concentration Versus Time Curve (AUC) of VX-670 and its Active Component in Plasma After Each DoseFrom Day 1 up to Day 168
Part A: Maximum Observed Concentration (Cmax) of VX-670 and its Active Component in PlasmaFrom Day 1 up to Day 42
Part B: Change in Splicing Index in Muscle BiopsyBaseline and at Day 15
Part B: Concentration of VX-670 and its Active Component in MuscleBaseline and at Day 15
Part A: Area Under the Concentration Versus Time Curve (AUC) of VX-670 and its Active Component in PlasmaFrom Day 1 up to Day 42
Part B: Maximum Observed Concentration (Cmax) of VX-670 and its Active Component in Plasma After Each DoseFrom Day 1 up to Day 168

Trial Locations

Locations (26)

Stanford Neuromuscular Research

🇺🇸

San Carlos, California, United States

University of Florida Clinical Research Center

🇺🇸

Gainesville, Florida, United States

University of Kansas Medical Center

🇺🇸

Fairway, Kansas, United States

Boston Children's Hospital

🇺🇸

Boston, Massachusetts, United States

Washington University School of Medicine / St. Louis Children's Hospital

🇺🇸

Saint Louis, Missouri, United States

Wake Forest Baptist Health

🇺🇸

Winston-Salem, North Carolina, United States

University of Pennsylvania

🇺🇸

Philadelphia, Pennsylvania, United States

Virginia Commonwealth University (Sanger Hall)

🇺🇸

Richmond, Virginia, United States

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

🇧🇪

Leuven, Belgium

McGIll University

🇨🇦

Montreal, Canada

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Stanford Neuromuscular Research
🇺🇸San Carlos, California, United States
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