MedPath

A Study Evaluating the Efficacy and Safety of Crovalimab Versus Eculizumab in Participants With Paroxysmal Nocturnal Hemoglobinuria (PNH) Not Previously Treated With Complement Inhibitors

Phase 3
Active, not recruiting
Conditions
Paroxysmal Nocturnal Hemoglobinuria
Interventions
Registration Number
NCT04434092
Lead Sponsor
Hoffmann-La Roche
Brief Summary

A study designed to evaluate the non-inferiority of crovalimab compared with eculizumab in participants with PNH who have not been previously treated with complement inhibitor therapy.

Detailed Description

Not available

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
204
Inclusion Criteria
  • Body weight ≥ 40 kg at screening (pediatric participants with body weight < 40 kg)
  • Willingness and ability to comply with all study visits and procedures
  • Documented diagnosis of PNH, confirmed by high sensitivity flow cytometry
  • LDH level ≥ 2x ULN at screening (as per local assessment)
  • Vaccination against Neisseria meningitidis serotypes A, C, W, and Y< 3 years prior to initiation of study treatment; or, if not previously done, vaccination administered no later than one week after the first drug administration
  • Women of childbearing potential: agreement to remain abstinent or use contraception during the treatment period and for 10.5 months after the final dose of crovalimab or for 3 months after the final dose of eculizumab (or longer if required by the local product label)
Exclusion Criteria
  • Current or previous treatment with a complement inhibitor
  • History of allogeneic bone marrow transplantation
  • History of Neisseria meningitidis infection within 6 months prior to screening and up to first study drug administration
  • History of myelodysplastic syndrome with Revised International Prognostic Scoring System (IPSS-R) prognostic risk categories of intermediate, high and very high
  • Pregnant or breastfeeding, or intending to become pregnant during the study, within 10.5 months after the final dose of crovalimab, or 3 months after the final dose of eculizumab (or longer if required by the local product label)
  • Participation in another interventional treatment study with an investigational agent or use of any experimental therapy within 28 days of screening or within 5 half-lives of that investigational product, whichever is greater
  • Concurrent disease, treatment, procedure or surgery, or abnormality in clinical laboratory tests that could interfere with the conduct of the study, may pose any additional risk for the participant, or would, in the opinion of the Investigator, preclude the participant's safe participation in and completion of the study
  • Splenectomy < 6 months before screening
  • Positive for Active Hepatitis B and C infection (HBV/HCV)
  • History of or ongoing cryoglobulinemia at screening

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Arm B (Eculizumab)CrovalimabParticipants will receive loading dose of eculizumab 600 mg on Days 1, 8, 15, and 22, followed by maintenance dose of 900 mg on Day 29 and every 2 weeks (Q2W) thereafter until 24 weeks. Participants may switch to receive crovalimab after 24 weeks of eculizumab treatment.
Arm B (Eculizumab)EculizumabParticipants will receive loading dose of eculizumab 600 mg on Days 1, 8, 15, and 22, followed by maintenance dose of 900 mg on Day 29 and every 2 weeks (Q2W) thereafter until 24 weeks. Participants may switch to receive crovalimab after 24 weeks of eculizumab treatment.
Arm A (Crovalimab)CrovalimabCrovalimab will be administered at an initial loading dose of 1000 milligrams (mg) (for participants with body weight between 40 and 100 kilograms \[kg\]) or 1500 mg (for participants with body weight ≥ 100 kg), as intravenous (IV) injection on Day 1 of Week 1 followed by four weekly subcutaneous (SC) injections of 340 mg starting on Day 2 of Week 1 and then once weekly (QW) at Weeks 2,3 and 4. Thereafter crovalimab will be administered, as SC injection, at a maintenance dose of 680 mg (for participants with body weight between 40 and 100 kg) or 1020 mg (for participants with body weight ≥ 100 kg) once every 4 weeks (Q4W) from Week 5 for a total of 24 weeks of study treatment. Participants may continue to receive crovalimab after 24 weeks of treatment up to maximum of 5 years.
Arm C (Crovalimab) (Exploratory)CrovalimabParticipants with a body weight ≥ 5 to \<12 kg will receive a loading series of crovalimab doses comprised of an IV dose on Day 1 of Week 1, followed by crovalimab SC dose on Day 2 Week 1. Maintenance doses will begin at Week 3 and will be administered Q2W, thereafter. Participants with a body weight ≥ 12 to \< 20 kg and ≥ 20 kg will receive a loading series of crovalimab doses comprised of an IV dose on Day 1 of Week 1, followed by weekly crovalimab SC doses for 4 weeks at Week 1 (Day 2) and then at Weeks 2, 3, and 4. Maintenance doses will begin at Week 5 and will be administered Q2W thereafter, for participants with a body weight ≥ 12 to \< 20 kg and Q4W thereafter, for participants with a body weight \> 20 kg. After 24 weeks of crovalimab treatment, participants who derive benefit from the drug may continue to receive crovalimab.
Primary Outcome Measures
NameTimeMethod
Percentage of Participants Who Achieve Transfusion Avoidance (TA)Baseline through Week 25

TA is defined as participants who are packed red blood cell (pRBC) transfusion-free and do not require transfusion per protocol-specified guidelines.

Percentage of Participants With Hemolysis ControlWeek 5 through Week 25

Measured by lactate dehydrogenase (LDH) ≤ 1.5 x upper limit of normal (ULN) (as measured at the central laboratory).

Secondary Outcome Measures
NameTimeMethod
Percentage of Participants With Breakthrough Hemolysis (BTH)Baseline through Week 25

BTH is defined as at least one new or worsening symptom or sign of intravascular hemolysis (fatigue, hemoglobinuria, abdominal pain, shortness of breath \[dyspnea\], anemia \[hemoglobin \< 10 grams per deciliter (g/dL)\], a major adverse vascular event \[MAVE; including thrombosis\], dysphagia, or erectile dysfunction) in the presence of elevated LDH ≥ 2 x ULN after prior reduction of LDH to ≤ 1.5 x ULN on treatment.

Percentage of Participants With Stabilization of HemoglobinBaseline through Week 25

Stabilized hemoglobin is defined as avoidance of a ≥ 2 g/dL decrease in hemoglobin level from baseline, in the absence of transfusion.

Mean Change in FatigueBaseline up to Week 25

Assessed by the Functional Assessment of Chronic Illness Therapy (FACIT)-Fatigue Questionnaire.

Percentage of Participants With Adverse Events (AEs)Up to 6 years

Determined according to National Cancer Institute (NCI) Common Terminology Criteria for Adverse Events, Version 5.

Percentage of Participants With Injection-site Reactions, Infusion-related Reactions, Hypersensitivity and Infections (Including Meningococcal Meningitis)Up to 6 years
Percentage of Participants With Clinical Manifestations of Drug-target-drug Complex (DTDC) Formation Amongst Those Participants Who Switched to Crovalimab Treatment From Eculizumab TreatmentUp to 6 years
Serum Concentrations of Crovalimab and Eculizumab Over TimeUp to 6 years
Change Over Time in Free C5 Concentration in Crovalimab-treated ParticipantsUp to 6 years
Observed Value in Reticulocyte Count (count/milliliters [mL])Up to 6 years
Observed Value in Free Hemoglobin and Haptoglobin (milligrams per deciliter [mg/dL])Up to 6 years
Change From Baseline in Free Hemoglobin and Haptoglobin (mg/dL)Baseline up to Week 25
Percentage of Participants With AEs Leading to Study Drug DiscontinuationUp to 6 years
Percentage of Participants With Anti-crovalimab AntibodiesUp to 6 years
Change in Pharmacodynamic (PD) Biomarkers Including Complement Activity (CH50) Over TimeUp to 6 years

Assessed by a Liposome Immunoassay (LIA) and total C5 concentration.

Change From Baseline in Reticulocyte Count (count/mL)Baseline up to Week 25

Trial Locations

Locations (61)

MTZ Clinical Research Powered by Pratia

🇵🇱

Warszawa, Poland

Centre Hospitalier Lyon Sud

🇫🇷

Pierre-Bénite, France

Universitaetsklinikum Ulm

🇩🇪

Ulm, Germany

Hospital Ampang

🇲🇾

Ampang, Selangor, Malaysia

The First Affiliated Hospital, Zhejiang University

🇨🇳

Hangzhou City, China

Jiangsu Province Hospital

🇨🇳

Nanjing, China

Organizacion Medica de Investigacion (OMI)

🇦🇷

Ciudad Autonoma Buenos Aires, Argentina

Huashan Hospital, Fudan University

🇨🇳

Shanghai, China

Hopital Claude Huriez - CHU Lille

🇫🇷

Lille cedex, France

University of Tsukuba Hospital

🇯🇵

Ibaraki, Japan

Samsung Medical Center

🇰🇷

Seoul, Korea, Republic of

Instituto Português de Oncologia de Lisboa Francisco Gentil, E.P.E.

🇵🇹

Lisboa, Portugal

Hospital General Universitario Gregorio Marañon

🇪🇸

Madrid, Spain

Maharaj Nakorn Chiang Mai Hospital

🇹🇭

Chiang Mai, Thailand

General Hospital of Thessaloniki G. Papanikolaou

🇬🇷

Thessaloniki, Greece

Tokyo Medical University Hospital

🇯🇵

Tokyo, Japan

Asan Medical Center

🇰🇷

Seoul, Korea, Republic of

Instituto Nacional de Ciencias Medicas y Nutricion Salvador Zubiran

🇲🇽

Ciudad de México, Mexico CITY (federal District), Mexico

Philippine General Hospital

🇵🇭

Manila, Philippines

Centro Hospitalar do Porto - Hospital de Santo António

🇵🇹

Porto, Portugal

Hospital Universitario de Gran Canaria Dr. Negrin

🇪🇸

Las Palmas de Gran Canaria, LAS Palmas, Spain

Hospital San Pedro de Alcantara

🇪🇸

Caceres, Spain

Siriraj Hospital

🇹🇭

Bangkok, Thailand

King Chulalongkorn Memorial Hospital

🇹🇭

Pathum Wan, Thailand

Ondokuz Mayis Univ. Med. Fac.

🇹🇷

Samsun, Turkey

Centro Integrado de Oncologia de Curitiba

🇧🇷

Curitiba, Paraná, Brazil

Beneficencia Portuguesa de Sao Paulo

🇧🇷

São Paulo, Brazil

Nanfang Hospital, Southern Medical University

🇨🇳

Guangzhou, China

Union Hospital Tongji Medical College Huazhong University of Science and Technology

🇨🇳

Wuhan City, China

Universitaetsklinkm

🇩🇪

Essen, Germany

Seoul National University Hospital

🇰🇷

Seoul, Korea, Republic of

Severance Hospital, Yonsei University Health System

🇰🇷

Seoul, Korea, Republic of

Vilnius University Hospital Santariskiu Clinics, Public Institution

🇱🇹

Vilnius, Lithuania

Hospital Raja Permaisuri Bainun

🇲🇾

Ipoh, Perak, Malaysia

*X*CEPHO - Centro de Estudos e Pesquisas em Hematologia e Oncologia

🇧🇷

Santo Andre, São Paulo, Brazil

Peking Union Medical College Hospital

🇨🇳

Beijing, China

Affiliated Hospital of Nantong University

🇨🇳

Nantong City, China

Sapporo Medical University Hospital

🇯🇵

Hokkaido, Japan

NTT Medical Center Tokyo

🇯🇵

Tokyo, Japan

St Lukes Medical Center

🇵🇭

Quezon, Philippines

Uniwersyteckie Centrum Kliniczne

🇵🇱

Gdansk, Poland

Samodzielny Publiczny Szpital Kliniczny nr 1

🇵🇱

Lublin, Poland

Centro Hospitalar do Baixo Vouga E.P.E. - Hospital de Aveiro

🇵🇹

Aveiro, Portugal

National University Hospital

🇸🇬

Singapore, Singapore

Hospital de Basurto

🇪🇸

Bilbao, Albacete, Spain

ICO Badalona - Hospital Universitari Germans Trias i Pujol

🇪🇸

Badalona, Barcelona, Spain

Hospital Universitario Clinico San Carlos

🇪🇸

Madrid, Spain

Chang Gung Medical Foundation - Kaohsiung

🇨🇳

Kaohisung, Taiwan

Global Trial Research Center S.A. de C.V.

🇲🇽

Monterrey, Nuevo LEON, Mexico

Szpital Uniwersytecki nr2 im. dr J. Biziela

🇵🇱

Bydgoszcz, Poland

Spitalul Universitar de Urgenta Bucuresti

🇷🇴

Bucuresti, Romania

Singapore General Hospital

🇸🇬

Singapore, Singapore

Hospital Universitario de Salamanca

🇪🇸

Salamanca, Spain

National Taiwan Universtiy Hospital

🇨🇳

Taipei, Taiwan

Medical Center OK!Clinic+

🇺🇦

Kyiv, KIEV Governorate, Ukraine

Amsterdam UMC, Locatie AMC

🇳🇱

Amsterdam, Netherlands

Mary Mediatrix Medical Center

🇵🇭

Lipa City, Philippines

Spitalul Clinic Municipal Filantropia Craiova

🇷🇴

Craiova, Romania

Hospital Universitario La Paz

🇪🇸

Madrid, Spain

St James University Hospital

🇬🇧

Leeds, United Kingdom

Kings College Hospital

🇬🇧

London, United Kingdom

© Copyright 2025. All Rights Reserved by MedPath