eusbijholteontstekingen en neuspoliepen bij volwassenen met taaislijmziekte.
Recruiting
- Conditions
- Cystic Fibrosis, nasal polyps, rhinosinusitis,Taaislijmziekte, neuspoliepen, rhinosinusitis
- Registration Number
- NL-OMON28476
- Lead Sponsor
- H.G.M. Heijerman, MD PhD & M.C. Berkhout, MDPulmonary DepartmentHaga Teaching Hospital, The Hague
- Brief Summary
/A
- Detailed Description
Not available
Recruitment & Eligibility
- Status
- Recruiting
- Sex
- Not specified
- Target Recruitment
- 100
Inclusion Criteria
1. Confirmed diagnose of Cystic Fibrosis based on genotyping or a positive sweat test;
2. Age equal to or above 18 years.
Exclusion Criteria
1. Gross immunodeficiency (congenital of acquired);
2. Congenital mucociliary problems other than CF (e.g. Primairy ciliary dyskinesia);
Study & Design
- Study Type
- Observational non invasive
- Study Design
- Not specified
- Primary Outcome Measures
Name Time Method Prevalence of rhinosinusitis and/or nasal polyps.
- Secondary Outcome Measures
Name Time Method 1. Disease specific quality of life (score on Rhinosinusitis Outcome Measure-31);<br /><br>2. Outcome of ENT examination (on a standardized form);<br /><br>3. Upper airway cultures (nasal lavage and middle meatal swabs);<br /><br>4. Sputum cultures;<br /><br>5. Nasal airway resistance;<br /><br>6. Computed tomography of sinuses and volume estimation of sinuses.