MedPath

A Study Evaluating the Efficacy and Safety of VX-445/Tezacaftor/Ivacaftor in Cystic Fibrosis Subjects, Homozygous for F508del

Phase 3
Completed
Conditions
Cystic Fibrosis
Interventions
Drug: TEZ/IVA
Drug: IVA
Registration Number
NCT04105972
Lead Sponsor
Vertex Pharmaceuticals Incorporated
Brief Summary

This study will evaluate the efficacy, safety, and pharmacodynamics of elexacaftor (ELX, VX-445) in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are homozygous for F508del.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
176
Inclusion Criteria
  • Homozygous for the F508del mutation (F/F)
  • Forced expiratory volume in 1 second (FEV1) value ≥40% and ≤90% of predicted mean for age, sex, and height

Key

Exclusion Criteria
  • Clinically significant cirrhosis with or without portal hypertension
  • Lung infection with organisms associated with a more rapid decline in pulmonary status
  • Solid organ or hematological transplantation

Other protocol defined Inclusion/Exclusion criteria may apply

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
ELX/TEZ/IVAIVAFollowing TEZ/IVA run-in period of 4 weeks, participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 24 weeks.
TEZ/IVATEZ/IVAFollowing TEZ/IVA run-in period of 4 weeks, participants received TEZ 100 milligrams (mg) once daily (qd)/IVA 150 mg every 12 hours (q12h) in the treatment period for 24 weeks.
TEZ/IVAIVAFollowing TEZ/IVA run-in period of 4 weeks, participants received TEZ 100 milligrams (mg) once daily (qd)/IVA 150 mg every 12 hours (q12h) in the treatment period for 24 weeks.
ELX/TEZ/IVAELX/TEZ/IVAFollowing TEZ/IVA run-in period of 4 weeks, participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 24 weeks.
Primary Outcome Measures
NameTimeMethod
Absolute Change in CF Questionnaire-Revised (CFQ-R) Respiratory Domain ScoreFrom Baseline Through Week 24

The CFQ-R is a validated participant-reported outcome measuring health-related quality of life for participants with cystic fibrosis. Respiratory domain assessed respiratory symptoms, score range: 0-100; higher scores indicating fewer symptoms and better health-related quality of life.

Secondary Outcome Measures
NameTimeMethod
Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)From Day 1 in the Treatment Period up to 28 Days After Last Dose of Study Drug or to the Completion of Study Participation Date, Whichever Occurs First (up to Week 28)
Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)From Baseline Through Week 24

FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration.

Absolute Change in Sweat Chloride (SwCl)From Baseline Through Week 24

Sweat samples were collected using an approved collection device.

Trial Locations

Locations (35)

Universitair Ziekenhuis Brussel - Campus Jette

🇧🇪

Brussels, Belgium

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

🇧🇪

Leuven, Belgium

Perth Children's Hospital

🇦🇺

Nedlands, Australia

Belfast City Hospital

🇬🇧

Belfast, United Kingdom

St. James University Hospital

🇬🇧

Leeds, United Kingdom

Leeds General Infirmary

🇬🇧

Leeds, West Yorkshire, United Kingdom

Queensland Children's Hospital

🇦🇺

South Brisbane, Australia

John Hunter Hospital & Hunter Medical Research Institute and John Hunter Children's Hospital

🇦🇺

New Lambton, Australia

The Prince Charles Hospital

🇦🇺

Chermside, Australia

Institute for Respiratory Health

🇦🇺

Nedlands, Australia

The Royal Children's Hospital

🇦🇺

Parkville, VIC, Australia

UZ Antwerpen

🇧🇪

Edegem, Belgium

Ruhrlandklinik Westdeutsches Lungenzentrum am Klinikum Essen

🇩🇪

Essen, Germany

Charite Paediatric Pulmonology Department

🇩🇪

Berlin, Germany

Universitatsklinikum Essen (AoR), Kinderklinik III, Abt. fur Pneumologie

🇩🇪

Essen, Germany

Johann Wolfgang Goethe University

🇩🇪

Frankfurt, Germany

Mukeviszidose-Zentrum am Universitatsklinikum Jena, Klinik fuer Kinder- und Jugendmedizin

🇩🇪

Jena, Germany

Universitaetsklinkum Koeln, CF-Studienzentrum

🇩🇪

Koeln, Germany

Klinikum Innenstadt, University of Munich

🇩🇪

München, Germany

University Hospitals Birmingham NHS Foundation Trust

🇬🇧

Birmingham, United Kingdom

University Hospitals Bristol NHS Foundation Trust, Bristol Royal Hospital

🇬🇧

Bristol, United Kingdom

Papworth Hospital NHS Foundation Trust, Papworth Everard

🇬🇧

Cambridge, United Kingdom

Western General Hospital

🇬🇧

Edinburgh, United Kingdom

Royal Devon and Exeter NHS Foundation Trust, Royal Devon and Exeter Hospital

🇬🇧

Exeter, United Kingdom

Clinical Research Facility, Queen Elizabeth University Hospital

🇬🇧

Glasgow, United Kingdom

Great Ormond Street Hospital for Sick Children

🇬🇧

London, United Kingdom

Alder Hey Children's Alder Hey Children's NHS Foundation Trust

🇬🇧

Liverpool, United Kingdom

London and St Bartholomew's Hospital

🇬🇧

London, United Kingdom

The University Hospital of South Manchester

🇬🇧

Manchester, United Kingdom

The Newcastle upon Tyne Hospitals NHS Foundation Trust, The Royal Victoria Infirmary

🇬🇧

Newcastle Upon Tyne, United Kingdom

Nottingham University Hospitals NHS Trust, Queens Medical Center

🇬🇧

Nottingham, United Kingdom

All Wales Adult Cystic Fibrosis Centre, University Hospital Llandough

🇬🇧

Penarth, United Kingdom

Southampton General Hospital

🇬🇧

Southampton, United Kingdom

Pneumologisches Studienzentrum Muenchen-West

🇩🇪

Muenchen, Germany

Universitair Ziekenhuis Gent

🇧🇪

Gent, Belgium

© Copyright 2025. All Rights Reserved by MedPath